Papillon-Lefèvre Syndrome: Diagnosis, Dental Management, and a Case Report
المؤلفون المشاركون
Noujeim, Ziad
Abou Chedid, Jean-Claude
Salameh, Michel
El-Outa, Abbass
المصدر
العدد
المجلد 2019، العدد 2019 (31 ديسمبر/كانون الأول 2019)، ص ص. 1-7، 7ص.
الناشر
Hindawi Publishing Corporation
تاريخ النشر
2019-04-21
دولة النشر
مصر
عدد الصفحات
7
التخصصات الرئيسية
الملخص EN
Aim.
This paper revisits Papillon-Lefèvre syndrome (PLS), addresses its diagnostic update and dental management, and reports a case of a 5-year-old Lebanese patient with consanguineously married parents.
Background.
PLS, also known as “keratoris palmoplantaris with periodontopathia” and “hyperkeratosis palmoplantaris with periodontosis,” is an extremely rare autosomal-recessive trait that combines a diffuse palmoplantar hyperkeratosis and a severe generalized, progressive prepubertal form of a precocious form of juvenile, aggressive periodontitis.
Case Description.
We are reporting a 5-year-old boy that sustained a spontaneous loss of all his primary teeth.
At consultation, he was under treatment for hyperkeratosis of his palms and soles.
Detailed family history of the child revealed that the patient’s parents, grandparents, and relatives were consanguineously married and two of his cousins displayed similar clinical signs (palmoplantar hyperkeratosis and premature loss of deciduous and most of the permanent teeth).
Conclusion.
PLS is an extremely rare disorder that usually becomes apparent from approximately 1-5 years of age.
Genetic counseling should always be suggested to parents of affected children, informing them of chances of their offspring having the inherited disease.
نمط استشهاد جمعية علماء النفس الأمريكية (APA)
Abou Chedid, Jean-Claude& Salameh, Michel& El-Outa, Abbass& Noujeim, Ziad. 2019. Papillon-Lefèvre Syndrome: Diagnosis, Dental Management, and a Case Report. Case Reports in Dentistry،Vol. 2019, no. 2019, pp.1-7.
https://search.emarefa.net/detail/BIM-1134618
نمط استشهاد الجمعية الأمريكية للغات الحديثة (MLA)
Abou Chedid, Jean-Claude…[et al.]. Papillon-Lefèvre Syndrome: Diagnosis, Dental Management, and a Case Report. Case Reports in Dentistry No. 2019 (2019), pp.1-7.
https://search.emarefa.net/detail/BIM-1134618
نمط استشهاد الجمعية الطبية الأمريكية (AMA)
Abou Chedid, Jean-Claude& Salameh, Michel& El-Outa, Abbass& Noujeim, Ziad. Papillon-Lefèvre Syndrome: Diagnosis, Dental Management, and a Case Report. Case Reports in Dentistry. 2019. Vol. 2019, no. 2019, pp.1-7.
https://search.emarefa.net/detail/BIM-1134618
نوع البيانات
مقالات
لغة النص
الإنجليزية
الملاحظات
Includes bibliographical references
رقم السجل
BIM-1134618
قاعدة معامل التأثير والاستشهادات المرجعية العربي "ارسيف Arcif"
أضخم قاعدة بيانات عربية للاستشهادات المرجعية للمجلات العلمية المحكمة الصادرة في العالم العربي
تقوم هذه الخدمة بالتحقق من التشابه أو الانتحال في الأبحاث والمقالات العلمية والأطروحات الجامعية والكتب والأبحاث باللغة العربية، وتحديد درجة التشابه أو أصالة الأعمال البحثية وحماية ملكيتها الفكرية. تعرف اكثر