In Vitro Contracture Test Results and Anaesthetic Management of a Patient with Emery-Dreifuss Muscular Dystrophy for Cardiac Transplantation

المؤلفون المشاركون

Wessig, Carsten
Aleksic, Ivan
Schimmer, Christoph
Roewer, Norbert
Leyh, Rainer
Lazarus, Marc
Johannsen, Stephan
Schuster, Frank

المصدر

Case Reports in Anesthesiology

العدد

المجلد 2012، العدد 2012 (31 ديسمبر/كانون الأول 2012)، ص ص. 1-4، 4ص.

الناشر

Hindawi Publishing Corporation

تاريخ النشر

2012-09-03

دولة النشر

مصر

عدد الصفحات

4

التخصصات الرئيسية

الطب البشري

الملخص EN

Emery-Dreifuss muscular dystrophy (EDMD) is a hereditary neuromuscular disorder characterized by slowly progressive muscle weakness, early contractures, and dilated cardiomyopathy.

We reported an uneventful general anaesthesia using total intravenous anaesthesia (TIVA) for cardiac transplantation in a 19-year-old woman suffering from EDMD.

In vitro contracture test results of two pectoralis major muscle bundles of the patient suggest that exposition to triggering agents does not induce a pathological sarcoplasmic calcium release in the lamin A/C phenotype.

However, due to the lack of evidence in the literature, we would recommend TIVA for patients with EDMD if general anaesthesia is required.

نمط استشهاد جمعية علماء النفس الأمريكية (APA)

Schuster, Frank& Wessig, Carsten& Schimmer, Christoph& Johannsen, Stephan& Lazarus, Marc& Aleksic, Ivan…[et al.]. 2012. In Vitro Contracture Test Results and Anaesthetic Management of a Patient with Emery-Dreifuss Muscular Dystrophy for Cardiac Transplantation. Case Reports in Anesthesiology،Vol. 2012, no. 2012, pp.1-4.
https://search.emarefa.net/detail/BIM-464792

نمط استشهاد الجمعية الأمريكية للغات الحديثة (MLA)

Schuster, Frank…[et al.]. In Vitro Contracture Test Results and Anaesthetic Management of a Patient with Emery-Dreifuss Muscular Dystrophy for Cardiac Transplantation. Case Reports in Anesthesiology No. 2012 (2012), pp.1-4.
https://search.emarefa.net/detail/BIM-464792

نمط استشهاد الجمعية الطبية الأمريكية (AMA)

Schuster, Frank& Wessig, Carsten& Schimmer, Christoph& Johannsen, Stephan& Lazarus, Marc& Aleksic, Ivan…[et al.]. In Vitro Contracture Test Results and Anaesthetic Management of a Patient with Emery-Dreifuss Muscular Dystrophy for Cardiac Transplantation. Case Reports in Anesthesiology. 2012. Vol. 2012, no. 2012, pp.1-4.
https://search.emarefa.net/detail/BIM-464792

نوع البيانات

مقالات

لغة النص

الإنجليزية

الملاحظات

Includes bibliographical references

رقم السجل

BIM-464792