Erdheim-Chester Disease Associated with Marginal Zone Lymphoma and Monoclonal Proteinemia

الملخص EN

Erdheim-Chester disease (ECD) is a rare non-Langerhans cell histiocytosis.

We report a fatal case of ECD with extensive cardiac involvement associated with a marginal zone lymphoma and monoclonal proteinemia in a young man.

This is the first reported association of ECD with a monoclonal gammopathy or a lymphoma.