Primary Sjogren’s Syndrome Presenting as Acute Interstitial PneumonitisHamman-Rich Syndrome
Joint Authors
Khan, Abidullah
Humayun, Mohammad
Haider, Iqbal
Ayub, Maimoona
Shah, Zakir
Ajmal, Fahad
Source
Issue
Vol. 2016, Issue 2016 (31 Dec. 2016), pp.1-4, 4 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2016-10-13
Country of Publication
Egypt
No. of Pages
4
Main Subjects
Abstract EN
A previously well, 45-year-old Pakistani lady was admitted to the medical unit on-call of Khyber Teaching Hospital (KTH) Peshawar with a 5-day history of fever, productive cough with copious mucoid sputum, dyspnea, and pleuritic chest pain.
She also complained of dry eyes, mouth, and vagina.
Her chest X-ray showed diffuse alveolar shadowing and arterial gas analysis confirmed type 1 respiratory failure.
Over the next few days, she deteriorated rapidly making an urgent transfer to the medical intensive care unit (MICU) necessary, where she was mechanically ventilated.
An HRCT followed by bronchoscopic biopsies made a diagnosis of acute interstitial pneumonitis (AIP), formerly known as Hamman-Rich syndrome.
She also turned out to be positive for both anti-SS-A/Ro and anti-SS-B/La antibodies along with a positive Schirmer’s test and lower lip biopsy.
She received intravenous steroids and supportive care.
The patient had a complete recovery after approximately three weeks’ stay in the hospital with lung function returning back to normal.
This is most probably the first ever case of primary Sjogren syndrome (pSjS) presenting as AIP, recovering completely in less than a month time.
American Psychological Association (APA)
Khan, Abidullah& Humayun, Mohammad& Haider, Iqbal& Ayub, Maimoona& Shah, Zakir& Ajmal, Fahad. 2016. Primary Sjogren’s Syndrome Presenting as Acute Interstitial PneumonitisHamman-Rich Syndrome. Case Reports in Medicine،Vol. 2016, no. 2016, pp.1-4.
https://search.emarefa.net/detail/BIM-1101100
Modern Language Association (MLA)
Khan, Abidullah…[et al.]. Primary Sjogren’s Syndrome Presenting as Acute Interstitial PneumonitisHamman-Rich Syndrome. Case Reports in Medicine No. 2016 (2016), pp.1-4.
https://search.emarefa.net/detail/BIM-1101100
American Medical Association (AMA)
Khan, Abidullah& Humayun, Mohammad& Haider, Iqbal& Ayub, Maimoona& Shah, Zakir& Ajmal, Fahad. Primary Sjogren’s Syndrome Presenting as Acute Interstitial PneumonitisHamman-Rich Syndrome. Case Reports in Medicine. 2016. Vol. 2016, no. 2016, pp.1-4.
https://search.emarefa.net/detail/BIM-1101100
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-1101100