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Primary Ewing’s Sarcoma of the Spine in a Two-Year-Old Boy
Joint Authors
Electricwala, Ali J.
Electricwala, Jaffer T.
Source
Issue
Vol. 2016, Issue 2016 (31 Dec. 2016), pp.1-4, 4 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2016-11-08
Country of Publication
Egypt
No. of Pages
4
Main Subjects
Abstract EN
Ewing’s Sarcoma (ES) is a highly malignant bone tumour.
It may involve any part of the skeleton but the most frequent parts are the ilium and diaphysis of femur and tibia (Alfeeli et al., 2005; Zhu et al., 2012).
Primary ES of the spine is extremely rare (Yan et al., 2011).
It accounts for only 3.5 to 14.9 percent of all primary bone sarcomas.
The age of presentation ranges from 12 to 24 years (median 21 years) (Ferguson, 1999; Sharafuddin et al., 1992; Klimo Jr.
et al., 2009).
We report an unusual case of primary ES of the spine in a two-year-old boy, who presented to us with paraparesis and features of cauda equina syndrome.
MRI scan showed a tumour mass arising from the pedicle of L4 vertebra invading the spinal canal.
Tc-99 bone scan showed increased tracer uptake in L4 vertebra and normal tracer uptake elsewhere in the skeleton.
After reaching the diagnosis of a space occupying lesion invading the lumber spinal canal, we performed a decompressive laminectomy and a biopsy was sent which confirmed the diagnosis of ES.
Immunohistochemistry showed tumour cells staining positive for CD-99 (specific stain for ES).
Gene testing showed an EWS-FLI 1 chimera.
Surgery was followed by good improvement in motor signs.
The child was then referred to a specialized oncotherapy centre for further treatment, radiation, and chemotherapy.
To the best of our knowledge, we are the first to report primary ES of the spine at the age of two years.
American Psychological Association (APA)
Electricwala, Ali J.& Electricwala, Jaffer T.. 2016. Primary Ewing’s Sarcoma of the Spine in a Two-Year-Old Boy. Case Reports in Orthopedics،Vol. 2016, no. 2016, pp.1-4.
https://search.emarefa.net/detail/BIM-1102100
Modern Language Association (MLA)
Electricwala, Ali J.& Electricwala, Jaffer T.. Primary Ewing’s Sarcoma of the Spine in a Two-Year-Old Boy. Case Reports in Orthopedics No. 2016 (2016), pp.1-4.
https://search.emarefa.net/detail/BIM-1102100
American Medical Association (AMA)
Electricwala, Ali J.& Electricwala, Jaffer T.. Primary Ewing’s Sarcoma of the Spine in a Two-Year-Old Boy. Case Reports in Orthopedics. 2016. Vol. 2016, no. 2016, pp.1-4.
https://search.emarefa.net/detail/BIM-1102100
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-1102100