Lipschütz Genital Ulceration as Initial Manifestation of Primary Sjögren’s Syndrome
Joint Authors
Borges, Augusta
de Castro Coelho, Filipa
Amaral, Maria
Correia, Lúcia
Nunes Campos, Maria João
Paula, Tereza
Borrego, Jorge
Source
Case Reports in Obstetrics and Gynecology
Issue
Vol. 2018, Issue 2018 (31 Dec. 2018), pp.1-4, 4 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2018-06-03
Country of Publication
Egypt
No. of Pages
4
Main Subjects
Abstract EN
Genital ulcers are challenging to any clinician and causes transcend many specialties.
Skin ulceration in patients with primary Sjögren’s syndrome is infrequent but an established feature of cutaneous involvement.
Although gynecological symptoms, such as vulvovaginal dryness, dyspareunia, and pruritus, are common in women with primary Sjögren’s syndrome, patients affected by vulvar ulcers are unknown.
We describe an exceptional case of necrotic aphthous-type vulvar ulceration as initial presentation of primary Sjögren’s syndrome that was possibly triggered by an infectious agent.
Successful healing was achieved with oral corticosteroids, despite some loss of labia minora and labia majora as sequelae of the necrotizing process.
Reactive acute genital ulcers (Lipschütz ulcers) should be considered as a possible manifestation of many autoimmune/inflammatory disorders, beyond the classic associations such as Behçet’s syndrome or Crohn’s disease.
American Psychological Association (APA)
de Castro Coelho, Filipa& Amaral, Maria& Correia, Lúcia& Nunes Campos, Maria João& Paula, Tereza& Borges, Augusta…[et al.]. 2018. Lipschütz Genital Ulceration as Initial Manifestation of Primary Sjögren’s Syndrome. Case Reports in Obstetrics and Gynecology،Vol. 2018, no. 2018, pp.1-4.
https://search.emarefa.net/detail/BIM-1145686
Modern Language Association (MLA)
de Castro Coelho, Filipa…[et al.]. Lipschütz Genital Ulceration as Initial Manifestation of Primary Sjögren’s Syndrome. Case Reports in Obstetrics and Gynecology No. 2018 (2018), pp.1-4.
https://search.emarefa.net/detail/BIM-1145686
American Medical Association (AMA)
de Castro Coelho, Filipa& Amaral, Maria& Correia, Lúcia& Nunes Campos, Maria João& Paula, Tereza& Borges, Augusta…[et al.]. Lipschütz Genital Ulceration as Initial Manifestation of Primary Sjögren’s Syndrome. Case Reports in Obstetrics and Gynecology. 2018. Vol. 2018, no. 2018, pp.1-4.
https://search.emarefa.net/detail/BIM-1145686
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-1145686