Diagnosing Arthrogryposis Multiplex Congenita : A Review
Joint Authors
Kalampokas, Theodoros
Kalampokas, Emmanouil
Sofoudis, Chrisostomos
Deligeoroglou, Efthymios
Botsis, Dimitrios
Source
ISRN Obstetrics and Gynecology
Issue
Vol. 2012, Issue 2012 (31 Dec. 2012), pp.1-6, 6 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2012-09-23
Country of Publication
Egypt
No. of Pages
6
Main Subjects
Abstract EN
Arthrogryposis multiplex congenita (AMC) refers either to a syndromic or to a nonsyndromic group of conditions with varied etiology and complex clinical features, including multiple congenital contractures in different body areas.
Its etiology still remains unclear but generally any cause that leads to reduced fetal movement may lead to congenital contractures and in severe cases to fetal akinesia deformation sequence (FADS).
It affects approximately 1 in 2-3000 live births with an approximately equal gender ratio.
There are many known subgroups of AMC differing in signs, symptoms, and causes.
The primary diagnosis is made when a lack of mobility and an abnormal position is noted in routine ultrasound scanning.
Early diagnosis, prenatal evaluation, and further surveillance via image scanning (ultrasound and MRI) give the opportunity for family counseling concerning neonatal morbidity and mortality and labor or delivery planning.
Better understanding of the ultrasound findings and the etiology of this clinical situation offers the opportunity for careful prenatal assessment.
American Psychological Association (APA)
Kalampokas, Emmanouil& Kalampokas, Theodoros& Sofoudis, Chrisostomos& Deligeoroglou, Efthymios& Botsis, Dimitrios. 2012. Diagnosing Arthrogryposis Multiplex Congenita : A Review. ISRN Obstetrics and Gynecology،Vol. 2012, no. 2012, pp.1-6.
https://search.emarefa.net/detail/BIM-458688
Modern Language Association (MLA)
Kalampokas, Emmanouil…[et al.]. Diagnosing Arthrogryposis Multiplex Congenita : A Review. ISRN Obstetrics and Gynecology No. 2012 (2012), pp.1-6.
https://search.emarefa.net/detail/BIM-458688
American Medical Association (AMA)
Kalampokas, Emmanouil& Kalampokas, Theodoros& Sofoudis, Chrisostomos& Deligeoroglou, Efthymios& Botsis, Dimitrios. Diagnosing Arthrogryposis Multiplex Congenita : A Review. ISRN Obstetrics and Gynecology. 2012. Vol. 2012, no. 2012, pp.1-6.
https://search.emarefa.net/detail/BIM-458688
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-458688