Single stage release of bilateral amniotic band syndrome

Abstract EN

We present a case of amniotic band syndrome, a rare entity, affecting both legs of a newborn.

It isthe first case managed at our institution.

Our approach is a single stage release.

At birth, the baby had deep constriction rings around both legs with distal lymphedema which was severe on the right side involving the distal portion of the ring; the vascularity was maintained bilaterally.

The right tibia was fractured due to the tight band.

Release of both bands was performed on the first day of life with primary closure.

At 2 weeks of life, the surgical wounds had healed.

At 6 months, it was noticed that the swelling of the right foot increased and the band recurred.

Repeat excision was performed and intra-medullary nailing of the tibia was inserted.

Amniotic band syndrome has wide implications on the quality of the life of the affected infant.

In-utero diagnosis of the condition is important for the management; however, in-utero release is associated with a high incidence of premature birth.

A staged release of the band is the most commonly used surgical method though single staged procedures have yielded favorable results.