IgG4-related systemic disease imaging findings and review of the literature

Joint Authors

Zibuni, Suha Haddad
Musa, Lina Menassa
Aun, Noel
Zarur, Yusuf
Abi Khalil, Samir
Smayra, Tariq
Musa, Ronald

Source

Journal Médical Libanais

Issue

Vol. 66, Issue 5 (31 Dec. 2018), pp.267-274, 8 p.

Publisher

Lebanese Order of Physicians

Publication Date

2018-12-31

Country of Publication

Lebanon

No. of Pages

8

Main Subjects

Medicine

Topics

Abstract EN

Immunoglobulin G4 (IgG4)-related systemic disease is a rare entity known for its pancreatic involvement that might be associated with other systemic lesions.

It usually presents as an autoimmune pancreatitis, sometimes mistaken for adenocarcinoma or cholangitis, salivary or lacrimal gland inflammation.

Kidney lesions, vasculitislike disease, and less frequently lung and gastric lesions can also occur.

Response to corticosteroids is highly suggestive.

We hereby present some computed tomography and magnetic resonance imaging findings of this disease

Abstract FRE

La maladie auto-immune à IgG4 est une entité rare qui atteint le pancréas mais également d’autres organes.

La pancréatite auto-immune à IgG4 est souvent confondue avec un adénocarcinome pancréatique en imagerie.

La maladie peut également se présenter sous forme de cholangite, d’inflammation des glandes salivaires ou lacrymales, d’hypodensités corticales rénales, de lésions mimant des vasculites, et, bien que moins souvent, d’atteintes pulmonaires ou gastriques.

La réponse aux corticostéroïdes est très suggestive de la maladie.

Nous présentons certains aspects radiologiques de la maladie et faisons une brève revue de la littérature

American Psychological Association (APA)

Musa, Lina Menassa& Zarur, Yusuf& Musa, Ronald& Abi Khalil, Samir& Smayra, Tariq& Zibuni, Suha Haddad…[et al.]. 2018. IgG4-related systemic disease imaging findings and review of the literature. Journal Médical Libanais،Vol. 66, no. 5, pp.267-274.
https://search.emarefa.net/detail/BIM-902220

Modern Language Association (MLA)

Musa, Lina Menassa…[et al.]. IgG4-related systemic disease imaging findings and review of the literature. Journal Médical Libanais Vol. 66, no. 5 (2018), pp.267-274.
https://search.emarefa.net/detail/BIM-902220

American Medical Association (AMA)

Musa, Lina Menassa& Zarur, Yusuf& Musa, Ronald& Abi Khalil, Samir& Smayra, Tariq& Zibuni, Suha Haddad…[et al.]. IgG4-related systemic disease imaging findings and review of the literature. Journal Médical Libanais. 2018. Vol. 66, no. 5, pp.267-274.
https://search.emarefa.net/detail/BIM-902220

Data Type

Journal Articles

Language

English

Notes

Includes bibliographical references : p. 273-274

Record ID

BIM-902220