IgG4-related systemic disease imaging findings and review of the literature
Joint Authors
Zibuni, Suha Haddad
Musa, Lina Menassa
Aun, Noel
Zarur, Yusuf
Abi Khalil, Samir
Smayra, Tariq
Musa, Ronald
Source
Issue
Vol. 66, Issue 5 (31 Dec. 2018), pp.267-274, 8 p.
Publisher
Publication Date
2018-12-31
Country of Publication
Lebanon
No. of Pages
8
Main Subjects
Topics
Abstract EN
Immunoglobulin G4 (IgG4)-related systemic disease is a rare entity known for its pancreatic involvement that might be associated with other systemic lesions.
It usually presents as an autoimmune pancreatitis, sometimes mistaken for adenocarcinoma or cholangitis, salivary or lacrimal gland inflammation.
Kidney lesions, vasculitislike disease, and less frequently lung and gastric lesions can also occur.
Response to corticosteroids is highly suggestive.
We hereby present some computed tomography and magnetic resonance imaging findings of this disease
Abstract FRE
La maladie auto-immune à IgG4 est une entité rare qui atteint le pancréas mais également d’autres organes.
La pancréatite auto-immune à IgG4 est souvent confondue avec un adénocarcinome pancréatique en imagerie.
La maladie peut également se présenter sous forme de cholangite, d’inflammation des glandes salivaires ou lacrymales, d’hypodensités corticales rénales, de lésions mimant des vasculites, et, bien que moins souvent, d’atteintes pulmonaires ou gastriques.
La réponse aux corticostéroïdes est très suggestive de la maladie.
Nous présentons certains aspects radiologiques de la maladie et faisons une brève revue de la littérature
American Psychological Association (APA)
Musa, Lina Menassa& Zarur, Yusuf& Musa, Ronald& Abi Khalil, Samir& Smayra, Tariq& Zibuni, Suha Haddad…[et al.]. 2018. IgG4-related systemic disease imaging findings and review of the literature. Journal Médical Libanais،Vol. 66, no. 5, pp.267-274.
https://search.emarefa.net/detail/BIM-902220
Modern Language Association (MLA)
Musa, Lina Menassa…[et al.]. IgG4-related systemic disease imaging findings and review of the literature. Journal Médical Libanais Vol. 66, no. 5 (2018), pp.267-274.
https://search.emarefa.net/detail/BIM-902220
American Medical Association (AMA)
Musa, Lina Menassa& Zarur, Yusuf& Musa, Ronald& Abi Khalil, Samir& Smayra, Tariq& Zibuni, Suha Haddad…[et al.]. IgG4-related systemic disease imaging findings and review of the literature. Journal Médical Libanais. 2018. Vol. 66, no. 5, pp.267-274.
https://search.emarefa.net/detail/BIM-902220
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references : p. 273-274
Record ID
BIM-902220