Behavioral assessment of children with spondylo-epi-metaphyseal dysplasias using the child behavior checklist

الملخص EN

SEMD is among the most important diseases tot cause disproportionate start stature and varying degrees of skeletal deformities (Temtamy et, al., 2007), These patients may also suffer from many associated behavioral problems.

The effects of these complications on the patient's behavior in previous studies were not definitive.

Patients And Methods: This study is a descriptive and exploratory study involving children with SEMDs recruited from the Limb Malformations and Skeletal Dysplasia Clinic (LMSDC), Center of Excellence of Human Genetics, National Research Centre (NRC).

The study included thirty seven cases.

Patients were classified according to the disease severity and associated complications into three groups, The child behavior checklist DSM- Oriented Scales for children translated by Dr.

Mona Elsheikh (Achenbach, 2001) was used to asset behavior problems of each child to determine the existence of any behavioral problems.

Results: The study included 37 cases of SEMDs, 7 cases of which had mild complications, 18 cases had moderate complications, and 12 cases had severe complications.

The number of male patients was 22 and 15 were females.

The study showed that these children suffer from several behavioral problems, especially the affective problems (62.1%).

Conclusion: This study emphasizes the importance of studying the behavioral problems associated with SEMDs winch result from short stature and skeletal deformities.

Early diagnosis is very important for referral of patients into specialists to begin prompt management in order to ease the associated behavioral problems.