Primary Amenorrhea, Aplastic Uterus, and a Functional Vagina: A Rare Case of Mayer-Rokitansky-Küster-Hauser Syndrome

المؤلفون المشاركون

Kirschen, Gregory W.
Semenyuk, Natalie

المصدر

Case Reports in Obstetrics and Gynecology

العدد

المجلد 2019، العدد 2019 (31 ديسمبر/كانون الأول 2019)، ص ص. 1-4، 4ص.

الناشر

Hindawi Publishing Corporation

تاريخ النشر

2019-05-28

دولة النشر

مصر

عدد الصفحات

4

التخصصات الرئيسية

الأمراض

الملخص EN

Background.

Müllerian agenesis, also known as Mayer-Rokitansky-Küster-Hauser syndrome (MRKHS), a failure of female urogenital development, typically results in a completely stenotic or rudimentary dimple vagina, both of which are generally nonfunctional in adulthood without mechanical dilation or surgical reconstruction.

Case.

A 20-year-old Tanner stage V heterosexual woman with normal sexual function since coitarche presented with a chief complaint of primary amenorrhea.

She was found to have aplastic uterine buds, absent endometrium/cervix, normal ovaries, and an unusually well-developed lower vagina, a rare presentation of MRKHS.

We discuss mechanisms by which the anomaly may have arisen.

Summary & Conclusion.

This case thus expands the clinical presentation of MRKHS to include a normal appearing vagina with intact sexual function from first sexual encounter, raising interesting questions about the basic underlying embryology.

نمط استشهاد جمعية علماء النفس الأمريكية (APA)

Kirschen, Gregory W.& Semenyuk, Natalie. 2019. Primary Amenorrhea, Aplastic Uterus, and a Functional Vagina: A Rare Case of Mayer-Rokitansky-Küster-Hauser Syndrome. Case Reports in Obstetrics and Gynecology،Vol. 2019, no. 2019, pp.1-4.
https://search.emarefa.net/detail/BIM-1141602

نمط استشهاد الجمعية الأمريكية للغات الحديثة (MLA)

Kirschen, Gregory W.& Semenyuk, Natalie. Primary Amenorrhea, Aplastic Uterus, and a Functional Vagina: A Rare Case of Mayer-Rokitansky-Küster-Hauser Syndrome. Case Reports in Obstetrics and Gynecology No. 2019 (2019), pp.1-4.
https://search.emarefa.net/detail/BIM-1141602

نمط استشهاد الجمعية الطبية الأمريكية (AMA)

Kirschen, Gregory W.& Semenyuk, Natalie. Primary Amenorrhea, Aplastic Uterus, and a Functional Vagina: A Rare Case of Mayer-Rokitansky-Küster-Hauser Syndrome. Case Reports in Obstetrics and Gynecology. 2019. Vol. 2019, no. 2019, pp.1-4.
https://search.emarefa.net/detail/BIM-1141602

نوع البيانات

مقالات

لغة النص

الإنجليزية

الملاحظات

Includes bibliographical references

رقم السجل

BIM-1141602