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Spondylocostal Dysostosis: A Literature Review and Case Report with Long-Term Follow-Up of a Conservatively Managed Patient
المؤلفون المشاركون
Southam, Brendan R.
Schumaier, Adam P.
Crawford, Alvin H.
المصدر
العدد
المجلد 2018، العدد 2018 (31 ديسمبر/كانون الأول 2018)، ص ص. 1-6، 6ص.
الناشر
Hindawi Publishing Corporation
تاريخ النشر
2018-03-22
دولة النشر
مصر
عدد الصفحات
6
التخصصات الرئيسية
الملخص EN
Introduction.
Patients with spondylocostal dysostosis (SCD) have congenital spine and rib deformities associated with frequently severe thoracic insufficiency and respiratory compromise.
The literature is largely composed of case reports and small cohorts, and there is little information regarding adults with this condition.
In this report, we describe the natural history of a conservatively treated patient and include quality-of-life issues such as childbearing, athletic participation, and occupational selection.
Case Presentation.
We present a patient with SCD who was conservatively treated by a single physician from birth for 31 years.
Our patient was capable of a reasonably good quality of life through adulthood, including participation in gymnastics and employment.
At age 18, she became pregnant and subsequently terminated the pregnancy due to obstetrical concerns for compromised respiration.
She has had intermittent respiratory complaints and occasionally experiences dyspnea with exertion, but this only has limited her during certain activities in the past three years.
Currently, she takes naproxen for chronic back pain with periodic exacerbations.
Discussion.
Other cases in the literature have described adult SCD patients who have received nonoperative treatment and achieved a wide range of functional outcomes.
This provides some limited evidence to suggest that select patients with SCD may be treated conservatively and achieve a reasonable quality of life.
However, close clinical follow-up with these patients is recommended, particularly early on, considering the high rates of infant morbidity and mortality.
Chest physiotherapy and early pulmonary care have been associated with favorable outcomes in infancy.
Surgery to increase thoracic volume and correct scoliosis has been shown in some cases to improve respiratory function.
Treatment depends on the degree of thoracic insufficiency and quality of life.
The natural history of SCD remains largely unknown, but some patients are capable of relatively favorable life spans, employment, and participation in athletics.
نمط استشهاد جمعية علماء النفس الأمريكية (APA)
Southam, Brendan R.& Schumaier, Adam P.& Crawford, Alvin H.. 2018. Spondylocostal Dysostosis: A Literature Review and Case Report with Long-Term Follow-Up of a Conservatively Managed Patient. Case Reports in Orthopedics،Vol. 2018, no. 2018, pp.1-6.
https://search.emarefa.net/detail/BIM-1147034
نمط استشهاد الجمعية الأمريكية للغات الحديثة (MLA)
Southam, Brendan R.…[et al.]. Spondylocostal Dysostosis: A Literature Review and Case Report with Long-Term Follow-Up of a Conservatively Managed Patient. Case Reports in Orthopedics No. 2018 (2018), pp.1-6.
https://search.emarefa.net/detail/BIM-1147034
نمط استشهاد الجمعية الطبية الأمريكية (AMA)
Southam, Brendan R.& Schumaier, Adam P.& Crawford, Alvin H.. Spondylocostal Dysostosis: A Literature Review and Case Report with Long-Term Follow-Up of a Conservatively Managed Patient. Case Reports in Orthopedics. 2018. Vol. 2018, no. 2018, pp.1-6.
https://search.emarefa.net/detail/BIM-1147034
نوع البيانات
مقالات
لغة النص
الإنجليزية
الملاحظات
Includes bibliographical references
رقم السجل
BIM-1147034
قاعدة معامل التأثير والاستشهادات المرجعية العربي "ارسيف Arcif"
أضخم قاعدة بيانات عربية للاستشهادات المرجعية للمجلات العلمية المحكمة الصادرة في العالم العربي
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