Mid-term outcome of Egyptian children post univentricular repair (experience of single center)‎

الملخص EN

-Background: More patients survive the operations for univentricular repair and the duration of follow up increases, the physicians are becoming increasingly aware of the late failure and the late complications of the surgery.

Objective: To evaluate the overall outcome of studied patients and to assess their functional status, and the occurrence of complications.

Patients and methods: This is a retrospective study; patients who underwent univentricular repair operations either Glenn or Fontan were included in the study.

The following data were collected: age, sex, type of the operation, and presence of early post operative complications.

The outcome was assessed by evaluating clinical status and growth of the patients during the follow-up visits.

Medical and surgical complications were retrieved.

Results: Thirty-nine patients who underwent univentricular repair operations either Glenn or Fontan were included from the pediatric post operative cardiac outpatient clinic.

Their age ranged from 2–18 years.

38 patients (97.4%) underwent Glenn operation followed by Fontan in 11 (27%) patients, 1 (2.6%) patient underwent Fontan without any previous operation and 4 (10.2%) patients underwent multistage palliation (prior operation to Glenn).

8 (20.5%) patients had early complications in the form of arrhythmia, bleeding, convulsions, and infection.

The general functional status of patients is good; growth curves are within the normal range in 30 (76.9%), and NYHA class I in 24 (61.5%) patients.

No late complications during follow-up and no mortality were documented.

Conclusion: Adequate post operative follow up is essential to improve midterm outcome of the patients.