Arrhythmogenic right ventricular cardiomyopathydysplasia (ARVC D)‎ : case presentation and literature review

الملخص EN

A case of Arrhythmogenic Right Ventricular Cardiomyopathy / Dysplasia (ARVC/D) has been presented.

ARVC / D is a disorder of RV myocardium which involves replacement of the myocardium with fibrofatty tissue.

The diagnosis was based on the findings of enlarged RV by echocardiography, ECG findings of : a) TWI (T- wave inversion)in V1,V2 & V3.

b) Epsilon wave in V1,V2, and more than 500 VEs/24 hour by Holter monitoring .Positive family history of sudden death in first degree relative (mother) was found.

This case supports the first report of 34 Cases of ARVC / D reported in Iraq and attracts the attention of the physicians, echocardiographers and cardiologist to the diagnosis of this fatal disorder where SCD (sudden cardiac death) can be prevented by ICD (implantable cardiac difebrelattor) implantation.