Brooke-Spiegler Syndrome : A Rare Entity

الملخص EN

Brooke-Spiegler syndrome is a rare entity.

It is an autosomal dominant syndrome in which multiple trichoepitheliomas, cylindromas, or other adnexal tumors are seen.

Very few cases of Brooke-Spiegler syndrome are reported in the literature.

We came across a 40 -year-old female in which multiple trichoepitheliomas and cylindromas were seen on scalp.

In view of clinical history and histopathological examination it was diagnosed as Brooke-Spiegler syndrome.

We report this case because of its rarity.