Extraskeletal Chondrosarcoma of Labium Majus

الملخص EN

Extraskeletal myxoid chondrosarcoma (ESMC) is a rare tumor seen more often in men.

It is seen to arise from soft tissue of lower extremity or buttocks.

We report a case of soft tissue swelling of left labium majus in a 66-year-old female.

Patient underwent wide excision with uneventful postoperative course.

Histopathology of specimen confirmed it to be ESMC.

Patient refused adjuvant therapy.

Followup of 1 year has shown her to be disease- and symptom- free.

Only two cases arising from vulva have been reported in literature .

This is the third case and first from Indian subcontinent.

A brief review of clinical features, diagnosis, treatment, and outcome of patients with extraskeletal chondrosarcoma is presented.