First Description of a Primitive Neuroectodermal Tumor Arising in the Nose

الملخص EN

We report the case of a 12-year-old girl, who consulted us with one-year history of an 8 mm nose lesion that was painless and firm upon palpation.

The lesion was resected conservatively.

Immunohistochemistry was in favor of a primitive neuroectodermal tumor (PNET)/Ewing’s sarcoma lesion, excluding epithelial, lymphoid, and other tumors.

After a second resection, our patient was referred to chemotherapy and has already undergone 9 cycles out of 14.

The patient is to date with no evidence of persistent or recurrent disease.

To our knowledge, this is the first description of a PNET arising in the nose.