Primary Ewing's Sarcoma of Frontoparietal Bone with Major Soft Tissue Extension : An Unusual Presentation and Review of the Literature

الملخص EN

An 11-year-old girl presented with progressively increasing swelling in scalp of 8-month duration with no neurological deficit.

Local examination showed a hard swelling that seemed to be arising from frontal bone.

General and systemic examination was normal.

MRI revealed a well-defined lytic lesion in left frontoparietal bone with a subgaleal component.

The patient was operated upon and excision of tumor with reconstruction of skull was done.

Histopathological examination showed a monomorphic small round cell tumor of bone infiltrating into the subcutaneous tissue.

Immunohistochemical stain showed diffuse immunopositivity for MIC-2 in tumor cells, thus final diagnosis of Ewing’s sarcoma was made.

The patient was kept for follow up for 3 months and had no symptoms.