Congenital Pulmonary Alveolar Proteinosis

الملخص EN

Pulmonary alveolar proteinosis (PAP) is a rare syndrome characterized by pulmonary surfactant accumulation within the alveolar spaces.

It occurs with a reported prevalence of 0.1 per 100,000 individuals.

Two clinically different pediatric types have been defined as congenital PAP which is fatal and a late-onset PAP which is similar to the adult form and less severe.

The clinical course of PAP is variable, ranging from spontaneous remission to respiratory failure.

Whole-lung lavage is the current standard treatment for PAP patients.

We report a new congenital case of PAP.