Pulmonary Hypertension in Portugal: First Data from a Nationwide Registry
Joint Authors
Baptista, Rui
Meireles, José
Agapito, Ana
Castro, Graça
Marinho da Silva, António
Shiang, Teresa
Gonçalves, Fabienne
Robalo-Martins, Susana
Nunes-Diogo, António
Reis, Abílio
Source
Issue
Vol. 2013, Issue 2013 (31 Dec. 2013), pp.1-8, 8 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2013-10-21
Country of Publication
Egypt
No. of Pages
8
Main Subjects
Abstract EN
Pulmonary arterial hypertension (PAH) is a rare disease that must be managed in specialized centers; therefore, the availability of epidemiological national data is critical.
Methods.
We conducted a prospective, observational, and multicenter registry with a joint collaboration from five centers from Portugal and included adult incident patients with PAH or chronic thromboembolic pulmonary hypertension (CTEPH).
Results.
Of the 79 patients enrolled in this study, 46 (58.2%) were classified as PAH and 33 patients (41.8%) as CTEPH.
PAH patients had a mean age of 43.4 ± 16.4 years.
Idiopathic PAH was the most common etiology (37%).
At presentation, PAH patients had elevated right atrial pressure (RAP) (7.7 ± 5.9 mmHg) and mean pulmonary vascular resistance (11.4 ± 6.5 Wood units), with a low cardiac index (2.7 ± 1.1 L·min−1·m−2); no patient was under selective pulmonary vasodilators; however, at follow-up, most patients were on single (50%), double (28%), or triple (9%) combination vasodilator therapy.
One-year survival was 93.5%, similar to CTEPH patients (93.9%), that were older (60.0 ± 12.5 years) and had higher RAP (11.0 ± 5.2 mmHg, P=0.015).
Conclusions.
We describe for the first time nationwide data on the diagnosis, management, and prognosis of PAH and CTEPH patients in Portugal.
Clinical presentation and outcomes are comparable with those reported on other national registries.
American Psychological Association (APA)
Baptista, Rui& Meireles, José& Agapito, Ana& Castro, Graça& Marinho da Silva, António& Shiang, Teresa…[et al.]. 2013. Pulmonary Hypertension in Portugal: First Data from a Nationwide Registry. BioMed Research International،Vol. 2013, no. 2013, pp.1-8.
https://search.emarefa.net/detail/BIM-1004437
Modern Language Association (MLA)
Baptista, Rui…[et al.]. Pulmonary Hypertension in Portugal: First Data from a Nationwide Registry. BioMed Research International No. 2013 (2013), pp.1-8.
https://search.emarefa.net/detail/BIM-1004437
American Medical Association (AMA)
Baptista, Rui& Meireles, José& Agapito, Ana& Castro, Graça& Marinho da Silva, António& Shiang, Teresa…[et al.]. Pulmonary Hypertension in Portugal: First Data from a Nationwide Registry. BioMed Research International. 2013. Vol. 2013, no. 2013, pp.1-8.
https://search.emarefa.net/detail/BIM-1004437
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-1004437