Desmoplastic Small Round Cell Tumor of Stomach
Joint Authors
al-Hussaini, Hussa
Abu-Zaid, Ahmed
Azzam, Ayman
AlNajjar, Asma
Amin, Tarek
Source
Case Reports in Gastrointestinal Medicine
Issue
Vol. 2013, Issue 2013 (31 Dec. 2013), pp.1-6, 6 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2013-06-06
Country of Publication
Egypt
No. of Pages
6
Main Subjects
Abstract EN
Desmoplastic small round cell tumor (DSRCT) is an extremely uncommon, highly aggressive, and malignant mesenchymal neoplasm of undetermined histogenesis.
Less than 200 case reports have been documented in literature so far.
Herein, we report a 26-year-old otherwise healthy female patient who presented with a 1-month history of epigastric pain.
On physical examination, a palpable, slightly mobile, and tender epigastric mass was detected.
All laboratory tests were normal.
A chest, abdominal, and pelvic contrast-enhanced computed tomography (CT) scans showed a 3.8 × 7.2 × 8.7 cm ill-defined mass, involving gastric fundus and extending into gastric cardia and lower gastroesophageal junction.
It was associated with multiple enlarged gastrohepatic lymph nodes; the largest measured 1.2 cm.
There was no evidence of ascites or retroperitoneal or mesenteric lymphatic metastases.
Patient underwent total gastrectomy with D2 lymphadenectomy, splenectomy, and antecolic Roux-en-Y esophagojejunal anastomosis.
Histopathological examination revealed coexpression of mesenchymal, epithelial, and neural markers.
The characteristic chromosomal translocation (t(11; 22)(p13; q12)) was demonstrated on fluorescence in situ hybridization (FISH) technique.
Diagnosis of DSRCT of stomach was confirmed.
Patient received no postoperative radiotherapy or chemotherapy.
A postoperative 3-month followup failed to show any recurrence.
In addition, a literature review on DSRCT is included.
American Psychological Association (APA)
Abu-Zaid, Ahmed& Azzam, Ayman& AlNajjar, Asma& al-Hussaini, Hussa& Amin, Tarek. 2013. Desmoplastic Small Round Cell Tumor of Stomach. Case Reports in Gastrointestinal Medicine،Vol. 2013, no. 2013, pp.1-6.
https://search.emarefa.net/detail/BIM-1005720
Modern Language Association (MLA)
Abu-Zaid, Ahmed…[et al.]. Desmoplastic Small Round Cell Tumor of Stomach. Case Reports in Gastrointestinal Medicine No. 2013 (2013), pp.1-6.
https://search.emarefa.net/detail/BIM-1005720
American Medical Association (AMA)
Abu-Zaid, Ahmed& Azzam, Ayman& AlNajjar, Asma& al-Hussaini, Hussa& Amin, Tarek. Desmoplastic Small Round Cell Tumor of Stomach. Case Reports in Gastrointestinal Medicine. 2013. Vol. 2013, no. 2013, pp.1-6.
https://search.emarefa.net/detail/BIM-1005720
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-1005720