Low-Grade Malignant Triton Tumor of the Neck: A Case Report and Review of the Literature

Abstract EN

Rhabdomyoblastic differentiation in a malignant peripheral nerve sheath tumor (MPNST) is termed malignant triton tumor (MTT), a rare neoplasm that poses a diagnostic dilemma in the differential diagnosis of neck masses and portends poor prognosis.

We report a sporadic case of MTT of the neck in a 23-year-old female.

We present the pathological findings.

Immunohistochemistry confirmed the neurogenic origin with S-100 expression and the rhabdomyoblastic differentiation with desmin and vimentin positivity.

Radical surgical excision was done.

After 4 years there were no signs of recurrence or distant metastasis.

The clinical, microscopic, and long-term follow-up of this case are consistent with those of a low-grade malignancy.