Desmoid-Type Fibromatosis of the Mesentery: Report of a Sporadic Case with Emphasis on Differential Diagnostic Problems
Joint Authors
Ferraro, Maria Jessica
Calabrini, Martina
Pennisi, Monica
Magro, Gaetano
Li Destri, Giovanni
Source
Issue
Vol. 2014, Issue 2014 (31 Dec. 2014), pp.1-7, 7 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2014-09-30
Country of Publication
Egypt
No. of Pages
7
Main Subjects
Abstract EN
Desmoid-type fibromatosis is a rare mesenchymal neoplasm with local aggressiveness.
The incidence of desmoid-type fibromatosis is 2–5/million/year with intra-abdominal fibromatosis, such as that which is reported in this clinical case, occurring only in 12–18% of cases.
After having analyzed the pathogenetic hypotheses of desmoid-type fibromatosis, the authors point out that the diagnosis of this disease, especially in the intra-abdominal form, is often late, specifically when highly demolitive interventions are needed or when the limits of radical surgery have been exceeded.
In the clinical case reported, the tumor was infiltrating both ileus and sigma.
The authors consider the differential diagnosis of desmoid-type fibromatosis, especially with GISTs, with regard to both the radiological preoperative diagnostic and histological studies on the surgical specimen.
Radical surgical excision is not always, for this disease, a sign of healing; in fact, even when the resection margins are negative, the incidence of recurrence is between 13 and 68%.
The average time of recurrence is between 15 and 24 months; in this case report, the patient, who has not been subjected to complementary therapies, is tumor-free for over 30 months since surgery; his prognosis may be satisfactory if we consider the negativity of resection margins, which in any case remains the most important prognostic factor.
American Psychological Association (APA)
Li Destri, Giovanni& Ferraro, Maria Jessica& Calabrini, Martina& Pennisi, Monica& Magro, Gaetano. 2014. Desmoid-Type Fibromatosis of the Mesentery: Report of a Sporadic Case with Emphasis on Differential Diagnostic Problems. Case Reports in Medicine،Vol. 2014, no. 2014, pp.1-7.
https://search.emarefa.net/detail/BIM-1034806
Modern Language Association (MLA)
Li Destri, Giovanni…[et al.]. Desmoid-Type Fibromatosis of the Mesentery: Report of a Sporadic Case with Emphasis on Differential Diagnostic Problems. Case Reports in Medicine No. 2014 (2014), pp.1-7.
https://search.emarefa.net/detail/BIM-1034806
American Medical Association (AMA)
Li Destri, Giovanni& Ferraro, Maria Jessica& Calabrini, Martina& Pennisi, Monica& Magro, Gaetano. Desmoid-Type Fibromatosis of the Mesentery: Report of a Sporadic Case with Emphasis on Differential Diagnostic Problems. Case Reports in Medicine. 2014. Vol. 2014, no. 2014, pp.1-7.
https://search.emarefa.net/detail/BIM-1034806
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-1034806