Anesthetic Management of a Child with Mitochondrial Neurogastrointestinal Encephalopathy
Joint Authors
Casarez, Vianey Q.
Zavala, Acsa M.
Owusu-Agyemang, Pascal
Hagan, Katherine
Source
Case Reports in Anesthesiology
Issue
Vol. 2015, Issue 2015 (31 Dec. 2015), pp.1-3, 3 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2015-06-01
Country of Publication
Egypt
No. of Pages
3
Main Subjects
Abstract EN
Mitochondrial neurogastrointestinal encephalomyopathy (MNGIE) is an autosomal recessive disorder associated with deficiency of thymidine phosphorylase (TP).
Associated manifestations include visual and hearing impairments, peripheral neuropathies, leukoencephalopathy, and malnutrition from concomitant gastrointestinal dysmotility and pseudoobstruction.
Given the altered metabolic state in these patients, specific consideration of medication selection is advised.
This case report will describe the anesthetic management used in a 10-year-old girl with MNGIE.
She had multiple anesthetics while undergoing allogeneic hematopoietic stem cell transplantation.
This case report will discuss the successful repeated use of the same anesthetic in this pediatric patient, with the avoidance of volatile anesthetic agents, propofol, and muscle relaxant.
American Psychological Association (APA)
Casarez, Vianey Q.& Zavala, Acsa M.& Owusu-Agyemang, Pascal& Hagan, Katherine. 2015. Anesthetic Management of a Child with Mitochondrial Neurogastrointestinal Encephalopathy. Case Reports in Anesthesiology،Vol. 2015, no. 2015, pp.1-3.
https://search.emarefa.net/detail/BIM-1058060
Modern Language Association (MLA)
Casarez, Vianey Q.…[et al.]. Anesthetic Management of a Child with Mitochondrial Neurogastrointestinal Encephalopathy. Case Reports in Anesthesiology No. 2015 (2015), pp.1-3.
https://search.emarefa.net/detail/BIM-1058060
American Medical Association (AMA)
Casarez, Vianey Q.& Zavala, Acsa M.& Owusu-Agyemang, Pascal& Hagan, Katherine. Anesthetic Management of a Child with Mitochondrial Neurogastrointestinal Encephalopathy. Case Reports in Anesthesiology. 2015. Vol. 2015, no. 2015, pp.1-3.
https://search.emarefa.net/detail/BIM-1058060
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-1058060