Rare Cause of Wide QRS Tachycardia

Abstract EN

Cardiac involvement is a well-known feature of neuromuscular diseases.

Most commonly cardiac manifestations occur later in the course of the disease.

Occasionally severe cardiac disease, including conduction disturbances, life-threatening arrhythmias, and cardiomyopathy, with its impact on prognosis, may be dissociated from peripheral myopathy.

We report a case of bundle branch reentrant ventricular tachycardia as primary manifestation of myotonic dystrophy and discuss associated diagnostic and treatment challenges.