Spontaneous Dissection of the Renal Artery in Vascular Ehlers-Danlos Syndrome
Joint Authors
Pereira, Filipa
Cardoso, Teresa
Sá, Paula
Source
Issue
Vol. 2015, Issue 2015 (31 Dec. 2015), pp.1-4, 4 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2015-06-15
Country of Publication
Egypt
No. of Pages
4
Main Subjects
Abstract EN
Ehlers-Danlos syndrome (EDS) is a rare heterogeneous group of connective tissue disorders.
The vascular type (vEDS) is an autosomal dominant disorder caused by heterozygous mutations in the COL3A1 gene predisposing to premature arterial, intestinal, or uterine rupture.
We report a case of a 38-year-old woman with a recent diagnosis of vEDS admitted in the Emergency Department with a suspicion of a pyelonephritis that evolved to a cardiopulmonary arrest.
A fatal retroperitoneal hematoma related with a haemorrhagic dissection of the right renal artery was found after emergency surgery.
This case highlights the need to be aware of the particular characteristics of vEDS, such as a severe vascular complication that can lead to a fatal outcome.
American Psychological Association (APA)
Pereira, Filipa& Cardoso, Teresa& Sá, Paula. 2015. Spontaneous Dissection of the Renal Artery in Vascular Ehlers-Danlos Syndrome. Case Reports in Critical Care،Vol. 2015, no. 2015, pp.1-4.
https://search.emarefa.net/detail/BIM-1058217
Modern Language Association (MLA)
Pereira, Filipa…[et al.]. Spontaneous Dissection of the Renal Artery in Vascular Ehlers-Danlos Syndrome. Case Reports in Critical Care No. 2015 (2015), pp.1-4.
https://search.emarefa.net/detail/BIM-1058217
American Medical Association (AMA)
Pereira, Filipa& Cardoso, Teresa& Sá, Paula. Spontaneous Dissection of the Renal Artery in Vascular Ehlers-Danlos Syndrome. Case Reports in Critical Care. 2015. Vol. 2015, no. 2015, pp.1-4.
https://search.emarefa.net/detail/BIM-1058217
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-1058217