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Successful Aortic Aneurysm Repair in a Woman with Severe von Willebrand (Type 3) Disease
Joint Authors
Campbell, Victoria
Marriott, Kevin
Stanbridge, Rex
Shlebak, Abdul
Source
Issue
Vol. 2015, Issue 2015 (31 Dec. 2015), pp.1-8, 8 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2015-04-19
Country of Publication
Egypt
No. of Pages
8
Main Subjects
Abstract EN
von Willebrand disease type 3 (VWD3) is a rare but the most severe form of von Willebrand disease; it is due to almost complete lack of von Willebrand factor activity (VWF:RCo).
It is inherited as autosomal recessive trait; whilst heterozygote carriers have mild, or no symptoms, patients with VWD3 show severe bleeding symptoms.
In the laboratory, this is characterised by undetectable VWF:Ag, VWF:RCo, and reduced levels of factor VIII < 0.02 IU/dL.
The bleeding is managed with von Willebrand/FVIII factor concentrate replacement therapy.
In this rare but challenging case we report on the successful excision and repair of an ascending aortic aneurysm following adequate VWF/FVIII factor concentrate replacement using Haemate-P.
American Psychological Association (APA)
Campbell, Victoria& Marriott, Kevin& Stanbridge, Rex& Shlebak, Abdul. 2015. Successful Aortic Aneurysm Repair in a Woman with Severe von Willebrand (Type 3) Disease. Case Reports in Hematology،Vol. 2015, no. 2015, pp.1-8.
https://search.emarefa.net/detail/BIM-1058631
Modern Language Association (MLA)
Campbell, Victoria…[et al.]. Successful Aortic Aneurysm Repair in a Woman with Severe von Willebrand (Type 3) Disease. Case Reports in Hematology No. 2015 (2015), pp.1-8.
https://search.emarefa.net/detail/BIM-1058631
American Medical Association (AMA)
Campbell, Victoria& Marriott, Kevin& Stanbridge, Rex& Shlebak, Abdul. Successful Aortic Aneurysm Repair in a Woman with Severe von Willebrand (Type 3) Disease. Case Reports in Hematology. 2015. Vol. 2015, no. 2015, pp.1-8.
https://search.emarefa.net/detail/BIM-1058631
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-1058631