Complete Surgical Resection of a Leiomyosarcoma Arising from the Inferior Vena Cava

Abstract EN

A 76-year-old Japanese man was referred to our hospital with chief complaint of right hypochondoralgia.

Abdominal ultrasound showed a retroperitoneal tumor in the suprarenal region of the right kidney.

Computed tomography revealed an enhanced lobular tumor with irregular, circumscribed, and indistinct border.

Ultrasound-guided biopsy was performed.

The tumor consisted of spindle-shaped cells with a giant nucleus and multinuclear cells.

The diagnosis was leiomyosarcoma by immunohistochemical staining.

The patient underwent surgery accessed by a right eighth intercostal thoracoabdominal incision.

The tumor was completely resected, accompanied by removal of the posterosuperior segment of the right hepatic lobe, right adrenal gland, and a portion of the inferior vena cava (IVC).

The histopathologic diagnosis was leiomyosarcoma arising from the IVC.

We present a rare case of a successfully managed leiomyosarcoma of the IVC.

This case suggests the importance of curative surgical resection of the tumor due to low efficacy of adjuvant chemotherapy for leiomyosarcoma.