Progressive Familial Intrahepatic Cholestasis: A Rare Cause of Cirrhosis in Young Adult Patients
Joint Authors
Source
Issue
Vol. 2015, Issue 2015 (31 Dec. 2015), pp.1-5, 5 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2015-06-02
Country of Publication
Egypt
No. of Pages
5
Main Subjects
Abstract EN
Hepatic cirrhosis is an important cause of morbidity and mortality.
An unusual case of cirrhosis and portal hypertension in an 18-year-old patient secondary to Progressive Intrahepatic Cholestasis is discussed.
The clinical and biochemical findings are discussed and a clinical approach to determining the underlying etiology of cirrhosis is outlined.
Significant complications of portal hypertension include ascites, spontaneous bacterial peritonitis, hepatorenal syndrome, varices, and hepatic encephalopathy.
A clinical approach to these complications of cirrhosis is presented.
Progressive Familial Intrahepatic Cholestasis (PFIC) is a rare congenital metabolic abnormality.
There are 3 subtypes and Type 3 PFIC commonly presents in late adolescence and early adulthood.
Clinical and laboratory findings as well as management for the condition are described.
American Psychological Association (APA)
Sun, Gavin R.& Burns, Michele. 2015. Progressive Familial Intrahepatic Cholestasis: A Rare Cause of Cirrhosis in Young Adult Patients. Case Reports in Medicine،Vol. 2015, no. 2015, pp.1-5.
https://search.emarefa.net/detail/BIM-1058841
Modern Language Association (MLA)
Sun, Gavin R.& Burns, Michele. Progressive Familial Intrahepatic Cholestasis: A Rare Cause of Cirrhosis in Young Adult Patients. Case Reports in Medicine No. 2015 (2015), pp.1-5.
https://search.emarefa.net/detail/BIM-1058841
American Medical Association (AMA)
Sun, Gavin R.& Burns, Michele. Progressive Familial Intrahepatic Cholestasis: A Rare Cause of Cirrhosis in Young Adult Patients. Case Reports in Medicine. 2015. Vol. 2015, no. 2015, pp.1-5.
https://search.emarefa.net/detail/BIM-1058841
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-1058841