Giant Congenital Melanocytic Nevi and Neurocutaneous Melanosis
Joint Authors
Araújo, Catarina
Resende, Cristina
Brito, Celeste
Pardal, Francisco
Source
Issue
Vol. 2015, Issue 2015 (31 Dec. 2015), pp.1-5, 5 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2015-02-04
Country of Publication
Egypt
No. of Pages
5
Main Subjects
Abstract EN
Introduction.
The major medical concern with giant congenital melanocytic nevi CMN is high risk of developing cutaneous melanoma, leptomeningeal melanoma, and neurocutaneous melanocytosis.
Case Report.
A 30-year-old woman with a giant congenital melanocytic nevus covering nearly the entire right thoracodorsal region and multiple disseminated melanocytic nevi presented with neurological symptoms.
Cerebral magnetic resonance imaging revealed a large expansive lesion in the left frontal region.
Postsurgically pathological diagnosis revealed characteristics of melanoma.
Immunohistochemical examination showed S100(+), HMB45(+), MelanA(+), and MiTF(+).
She received radiotherapy with temozolomide followed by two more chemotherapy cycles with temozolomide.
She followed a rapidly progressive course, reflecting widespread leptomeningeal infiltration, and she died of multiorgan failure seven months after diagnosis of cerebral melanoma.
Discussion.
This patient was diagnosed as having a neurocutaneous melanosis with malignant widespread leptomeningeal infiltration.
Diffuse spinal involvement is unusual and is described in only another patient.
American Psychological Association (APA)
Araújo, Catarina& Resende, Cristina& Pardal, Francisco& Brito, Celeste. 2015. Giant Congenital Melanocytic Nevi and Neurocutaneous Melanosis. Case Reports in Medicine،Vol. 2015, no. 2015, pp.1-5.
https://search.emarefa.net/detail/BIM-1058867
Modern Language Association (MLA)
Araújo, Catarina…[et al.]. Giant Congenital Melanocytic Nevi and Neurocutaneous Melanosis. Case Reports in Medicine No. 2015 (2015), pp.1-5.
https://search.emarefa.net/detail/BIM-1058867
American Medical Association (AMA)
Araújo, Catarina& Resende, Cristina& Pardal, Francisco& Brito, Celeste. Giant Congenital Melanocytic Nevi and Neurocutaneous Melanosis. Case Reports in Medicine. 2015. Vol. 2015, no. 2015, pp.1-5.
https://search.emarefa.net/detail/BIM-1058867
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-1058867