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The Myotonic Plot Thickens: Electrical Myotonia in Antimuscle-Specific Kinase Myasthenia Gravis
Joint Authors
Magnussen, Marcus
Harrison, Taylor B.
Karakis, Ioannis
Source
Case Reports in Neurological Medicine
Issue
Vol. 2015, Issue 2015 (31 Dec. 2015), pp.1-4, 4 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2015-12-03
Country of Publication
Egypt
No. of Pages
4
Main Subjects
Abstract EN
Electrical myotonia is known to occur in a number of inherited and acquired disorders including myotonic dystrophies, channelopathies, and metabolic, toxic, and inflammatory myopathies.
Yet, electrical myotonia in myasthenia gravis associated with antibodies against muscle-specific tyrosine kinase (MuSK) has not been previously reported.
We describe two such patients, both of whom had a typical presentation of proximal muscle weakness with respiratory failure in the context of a significant electrodecrement in repetitive nerve stimulation.
In both cases, concentric needle examination revealed electrical myotonia combined with myopathic motor unit morphology and early recruitment.
These findings suggest that MuSK myasthenia should be included within the differential diagnosis of disorders with electrical myotonia.
American Psychological Association (APA)
Magnussen, Marcus& Karakis, Ioannis& Harrison, Taylor B.. 2015. The Myotonic Plot Thickens: Electrical Myotonia in Antimuscle-Specific Kinase Myasthenia Gravis. Case Reports in Neurological Medicine،Vol. 2015, no. 2015, pp.1-4.
https://search.emarefa.net/detail/BIM-1059002
Modern Language Association (MLA)
Magnussen, Marcus…[et al.]. The Myotonic Plot Thickens: Electrical Myotonia in Antimuscle-Specific Kinase Myasthenia Gravis. Case Reports in Neurological Medicine No. 2015 (2015), pp.1-4.
https://search.emarefa.net/detail/BIM-1059002
American Medical Association (AMA)
Magnussen, Marcus& Karakis, Ioannis& Harrison, Taylor B.. The Myotonic Plot Thickens: Electrical Myotonia in Antimuscle-Specific Kinase Myasthenia Gravis. Case Reports in Neurological Medicine. 2015. Vol. 2015, no. 2015, pp.1-4.
https://search.emarefa.net/detail/BIM-1059002
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-1059002