Endometrioid Paraovarian Borderline Cystic Tumor in an Infant with Proteus Syndrome
Joint Authors
Vasquez, Liliana
Tello, Mariela
Maza, Ivan
Oscanoa, Monica
Dueñas, Milagros
Castro, Haydee
Latorre, Alan
Source
Case Reports in Oncological Medicine
Issue
Vol. 2015, Issue 2015 (31 Dec. 2015), pp.1-6, 6 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2015-10-19
Country of Publication
Egypt
No. of Pages
6
Main Subjects
Abstract EN
Ovarian and paraovarian neoplasms are uncommon in children, mainly originating from germ cell tumors and, least frequently, epithelial tumors.
There is an association between genital tract tumors and Proteus syndrome, a rare, sporadic, and progressive entity, characterized by a postnatal overgrowth in several tissues caused by a mosaic mutation in the AKT1 gene.
We describe a 20-month-old asymptomatic infant with Proteus syndrome who developed an endometrioid paraovarian borderline cystic tumor.
This is the youngest patient so far reported in the literature with this rare syndrome and an adnexal tumor of borderline malignancy.
A total of nine patients have been described with female tract tumors and associated Proteus syndrome, which includes bilateral ovarian cystadenomas and other benign masses.
A paraovarian neoplasm is extremely rare in children and could be considered a criterion for Proteus syndrome.
Standardized staging and treatment of these tumors are not well established; however, most authors conclude that these neoplasms must be treated as their ovarian counterparts.
American Psychological Association (APA)
Vasquez, Liliana& Tello, Mariela& Maza, Ivan& Oscanoa, Monica& Dueñas, Milagros& Castro, Haydee…[et al.]. 2015. Endometrioid Paraovarian Borderline Cystic Tumor in an Infant with Proteus Syndrome. Case Reports in Oncological Medicine،Vol. 2015, no. 2015, pp.1-6.
https://search.emarefa.net/detail/BIM-1059273
Modern Language Association (MLA)
Vasquez, Liliana…[et al.]. Endometrioid Paraovarian Borderline Cystic Tumor in an Infant with Proteus Syndrome. Case Reports in Oncological Medicine No. 2015 (2015), pp.1-6.
https://search.emarefa.net/detail/BIM-1059273
American Medical Association (AMA)
Vasquez, Liliana& Tello, Mariela& Maza, Ivan& Oscanoa, Monica& Dueñas, Milagros& Castro, Haydee…[et al.]. Endometrioid Paraovarian Borderline Cystic Tumor in an Infant with Proteus Syndrome. Case Reports in Oncological Medicine. 2015. Vol. 2015, no. 2015, pp.1-6.
https://search.emarefa.net/detail/BIM-1059273
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-1059273