Bilateral Sturge-Weber and Phakomatosis Pigmentovascularis with Glaucoma, an Overlap Syndrome
Joint Authors
Dada, Tanuj
Patil, Bharat
Sinha, Gautam
Nayak, Bhagabat
Sharma, Reetika
Kumari, Sadhana
Source
Case Reports in Ophthalmological Medicine
Issue
Vol. 2015, Issue 2015 (31 Dec. 2015), pp.1-3, 3 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2015-05-06
Country of Publication
Egypt
No. of Pages
3
Main Subjects
Abstract EN
Aim.
To report a case of bilateral Sturge-Weber and Phakomatosis pigmentovascularis with secondary glaucoma in a child.
Method.
Case report.
Results.
A 4-year-old male child was referred to us for control of intraocular pressure (IOP).
Sleeping IOP was 36 mm Hg in right eye and 28 mm Hg in the left eye.
The sclera of both the eyes showed bluish black pigmentation—melanosis bulbi.
Fundus examination of both eyes showed diffuse choroidal hemangiomas with glaucomatous cupping.
Nevus flammeus was present on both sides of face along all the 3 divisions of trigeminal nerve with overlying hypertrophy of skin and on left forearm.
Nevus fuscocaeruleus was present on upper trunk.
All skin lesions were present since birth and were stationary in nature.
CT scan of head revealed left-sided cerebral atrophy.
Intraocular pressure was controlled after treatment with topical antiglaucoma medications.
Pulsed Dye Laser has been advised by dermatologist for skin lesions.
Patient has been advised for regular follow-up.
Conclusion.
The two overlapping dermatological disorders and their association with glaucoma are a rare entity.
Management should be targeted both for dermatological and eye conditions.
American Psychological Association (APA)
Patil, Bharat& Sinha, Gautam& Nayak, Bhagabat& Sharma, Reetika& Kumari, Sadhana& Dada, Tanuj. 2015. Bilateral Sturge-Weber and Phakomatosis Pigmentovascularis with Glaucoma, an Overlap Syndrome. Case Reports in Ophthalmological Medicine،Vol. 2015, no. 2015, pp.1-3.
https://search.emarefa.net/detail/BIM-1059342
Modern Language Association (MLA)
Patil, Bharat…[et al.]. Bilateral Sturge-Weber and Phakomatosis Pigmentovascularis with Glaucoma, an Overlap Syndrome. Case Reports in Ophthalmological Medicine No. 2015 (2015), pp.1-3.
https://search.emarefa.net/detail/BIM-1059342
American Medical Association (AMA)
Patil, Bharat& Sinha, Gautam& Nayak, Bhagabat& Sharma, Reetika& Kumari, Sadhana& Dada, Tanuj. Bilateral Sturge-Weber and Phakomatosis Pigmentovascularis with Glaucoma, an Overlap Syndrome. Case Reports in Ophthalmological Medicine. 2015. Vol. 2015, no. 2015, pp.1-3.
https://search.emarefa.net/detail/BIM-1059342
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-1059342