Original Solution for Middle Ear Implant and AnestheticSurgical Management in a Child with Severe Craniofacial Dysmorphism

Abstract EN

We describe the novel solution adopted in positioning middle ear implant in a child with bilateral congenital aural atresia and craniofacial dysmorphism that have posed a significant challenge for the safe and correct management of deafness.

A five-year-old child, affected by a rare congenital disease (Van Maldergem Syndrome), suffered from conductive hearing loss.

Conventional skin-drive bone-conduction device, attached with a steel spring headband, has been applied but auditory restoration was not optimal.

The decision made was to position Vibrant Soundbridge, a middle ear implant, with an original surgical application due to hypoplasia of the tympanic cavity.

Intubation procedure was complicated due to child craniofacial deformities.

Postoperative hearing rehabilitation involved a multidisciplinary team, showing improved social skills and language development.