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Sinus Venosus Atrial Septal Defect Complicated by Eisenmenger Syndrome and the Role of Vasodilator Therapy
Joint Authors
Gedela, M.
Anuwatworn, Amornpol
Bendaly, Edgard
Prescott-Focht, Julia A.
Yee, Jimmy
Clark, Richard
Jonsson, Orvar
Source
Issue
Vol. 2016, Issue 2016 (31 Dec. 2016), pp.1-5, 5 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2016-11-14
Country of Publication
Egypt
No. of Pages
5
Main Subjects
Abstract EN
Sinus venosus atrial septal defect is a rare congenital, interatrial communication defect at the junction of the right atrium and the vena cava.
It accounts for 5–10% of cases of all atrial septal defects.
Due to the rare prevalence and anatomical complexity, diagnosing sinus venous atrial septal defects poses clinical challenges which may delay diagnosis and treatment.
Advanced cardiac imaging studies are useful tools to diagnose this clinical entity and to delineate the anatomy and any associated communications.
Surgical correction of the anomaly is the primary treatment.
We discuss a 43-year-old Hispanic female patient who presented with dyspnea and hypoxia following a laparoscopic myomectomy.
She had been diagnosed with peripartum cardiomyopathy nine years ago at another hospital.
Transesophageal echocardiography and computed tomographic angiography of the chest confirmed a diagnosis of sinus venosus atrial septal defect.
She was also found to have pulmonary arterial hypertension and Eisenmenger syndrome.
During a hemodynamic study, she responded to vasodilator and she was treated with Ambrisentan and Tadalafil.
After six months, her symptoms improved and her pulmonary arterial hypertension decreased.
We also observed progressive reversal of the right-to-left shunt.
This case illustrates the potential benefit of vasodilator therapy in reversing Eisenmenger physiology, which may lead to surgical repair of the atrial septal defect as the primary treatment.
American Psychological Association (APA)
Anuwatworn, Amornpol& Gedela, M.& Bendaly, Edgard& Prescott-Focht, Julia A.& Yee, Jimmy& Clark, Richard…[et al.]. 2016. Sinus Venosus Atrial Septal Defect Complicated by Eisenmenger Syndrome and the Role of Vasodilator Therapy. Case Reports in Cardiology،Vol. 2016, no. 2016, pp.1-5.
https://search.emarefa.net/detail/BIM-1100390
Modern Language Association (MLA)
Anuwatworn, Amornpol…[et al.]. Sinus Venosus Atrial Septal Defect Complicated by Eisenmenger Syndrome and the Role of Vasodilator Therapy. Case Reports in Cardiology No. 2016 (2016), pp.1-5.
https://search.emarefa.net/detail/BIM-1100390
American Medical Association (AMA)
Anuwatworn, Amornpol& Gedela, M.& Bendaly, Edgard& Prescott-Focht, Julia A.& Yee, Jimmy& Clark, Richard…[et al.]. Sinus Venosus Atrial Septal Defect Complicated by Eisenmenger Syndrome and the Role of Vasodilator Therapy. Case Reports in Cardiology. 2016. Vol. 2016, no. 2016, pp.1-5.
https://search.emarefa.net/detail/BIM-1100390
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-1100390