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Reactive Pulmonary Capillary Hemangiomatosis and Pulmonary Veno-Occlusive Disease in a Patient with Repaired Scimitar Syndrome
Joint Authors
Vrugt, B.
Güttinger, Eva
Speich, Rudolf
Ulrich, Silvia
Schwitz, Fabienne
Huber, Lars C.
Arrigo, Mattia
Source
Issue
Vol. 2016, Issue 2016 (31 Dec. 2016), pp.1-5, 5 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2016-03-16
Country of Publication
Egypt
No. of Pages
5
Main Subjects
Abstract EN
Pulmonary capillary hemangiomatosis (PCH) is a rare histological substrate within the spectrum of pulmonary arterial hypertension that possibly represents an unusual manifestation of pulmonary veno-occlusive disease (PVOD).
One of the histological hallmarks of PCH is the proliferation of pulmonary capillaries in the alveolar septa that infiltrate adjacent structures such as bronchioles, vessels, and visceral pleura.
The hyperplastic process involving the smallest vessels of the pulmonary vascular bed might reflect uncontrolled angiogenesis, but whether this vascular proliferation is idiopathic or, conversely, a reactive process remains to be elucidated.
Here we discuss the pathogenesis of PCH exemplified by the first reported case of a young patient with repaired scimitar syndrome that developed unilateral PCH.
American Psychological Association (APA)
Güttinger, Eva& Vrugt, B.& Speich, Rudolf& Ulrich, Silvia& Schwitz, Fabienne& Arrigo, Mattia…[et al.]. 2016. Reactive Pulmonary Capillary Hemangiomatosis and Pulmonary Veno-Occlusive Disease in a Patient with Repaired Scimitar Syndrome. Case Reports in Cardiology،Vol. 2016, no. 2016, pp.1-5.
https://search.emarefa.net/detail/BIM-1100411
Modern Language Association (MLA)
Güttinger, Eva…[et al.]. Reactive Pulmonary Capillary Hemangiomatosis and Pulmonary Veno-Occlusive Disease in a Patient with Repaired Scimitar Syndrome. Case Reports in Cardiology No. 2016 (2016), pp.1-5.
https://search.emarefa.net/detail/BIM-1100411
American Medical Association (AMA)
Güttinger, Eva& Vrugt, B.& Speich, Rudolf& Ulrich, Silvia& Schwitz, Fabienne& Arrigo, Mattia…[et al.]. Reactive Pulmonary Capillary Hemangiomatosis and Pulmonary Veno-Occlusive Disease in a Patient with Repaired Scimitar Syndrome. Case Reports in Cardiology. 2016. Vol. 2016, no. 2016, pp.1-5.
https://search.emarefa.net/detail/BIM-1100411
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-1100411