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Avoidable Compartment Syndrome! High Index of Suspicion for a Newly Presenting Haemophiliac: A Case Series
Joint Authors
Niblock, A.
Donnelly, K.
Sayers, F.
Winter, P.
Benson, G.
Source
Case Reports in Emergency Medicine
Issue
Vol. 2016, Issue 2016 (31 Dec. 2016), pp.1-6, 6 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2016-05-31
Country of Publication
Egypt
No. of Pages
6
Main Subjects
Abstract EN
Bleeding disorders can present at any age and vary in their severity.
Haemophilia, which is characterised by its x-linked recessive inheritance, can present with a spontaneous mutation and therefore no family history will be evident.
Three cases of trauma induced thigh haematomas as an initial presenting feature for people with haemophilia are discussed.
The cases highlight the importance of a coagulation screen if the patients bleeding phenotype does not match the injury sustained.
An isolated prolonged APTT with no offending anticoagulant cause should always be investigated to look for underlying haemophilia.
Interestingly the cases demonstrate the limitations of a coagulation screen.
Factor VIII being an acute phase reactant can result in the fact that the initial coagulation screen may be temporarily normal.
Therefore, if there is a high index of suspicion for a bleeding disorder, consider repeating the coagulation screen and seeking haematology opinion.
Early diagnosis and appropriate specific factor replacement for an injured haemophiliac prevent haematomas expanding thus avoiding potential complications like compartment syndrome or unnecessary surgical input.
American Psychological Association (APA)
Niblock, A.& Donnelly, K.& Sayers, F.& Winter, P.& Benson, G.. 2016. Avoidable Compartment Syndrome! High Index of Suspicion for a Newly Presenting Haemophiliac: A Case Series. Case Reports in Emergency Medicine،Vol. 2016, no. 2016, pp.1-6.
https://search.emarefa.net/detail/BIM-1100719
Modern Language Association (MLA)
Niblock, A.…[et al.]. Avoidable Compartment Syndrome! High Index of Suspicion for a Newly Presenting Haemophiliac: A Case Series. Case Reports in Emergency Medicine No. 2016 (2016), pp.1-6.
https://search.emarefa.net/detail/BIM-1100719
American Medical Association (AMA)
Niblock, A.& Donnelly, K.& Sayers, F.& Winter, P.& Benson, G.. Avoidable Compartment Syndrome! High Index of Suspicion for a Newly Presenting Haemophiliac: A Case Series. Case Reports in Emergency Medicine. 2016. Vol. 2016, no. 2016, pp.1-6.
https://search.emarefa.net/detail/BIM-1100719
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-1100719