![](/images/graphics-bg.png)
Splenic Involvement in Hereditary Hemorrhagic Telangiectasia
Joint Authors
Sato, Kota
Kato, Shunsuke
Ohtsukasa, Shunro
Kawachi, Yasuyuki
Nagano, Hiroto
Takamatsu, Susumu
Source
Issue
Vol. 2016, Issue 2016 (31 Dec. 2016), pp.1-4, 4 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2016-10-11
Country of Publication
Egypt
No. of Pages
4
Main Subjects
Abstract EN
A 33-year-old man who presented with prolonged epigastric pain was referred to our hospital.
He had experienced recurrent epistaxis and had a family history of hereditary hemorrhagic telangiectasia.
Computed tomography and magnetic resonance imaging revealed splenomegaly and a 9 cm hypervascular mass in his spleen.
Computed tomography also showed a pulmonary arteriovenous malformation and heterogeneous enhancement of the liver parenchyma, suggesting the presence of arteriosystemic shunts and telangiectases.
Based on these findings, the patient was definitely diagnosed with hereditary hemorrhagic telangiectasia according to Curaçao criteria.
He underwent splenectomy, and his symptoms disappeared after surgery.
Pathological examination of the resected specimen revealed that the hypervascular lesion of the spleen was not a tumor but was composed of abnormal vessels associated with hereditary hemorrhagic telangiectasia.
Symptomatic splenic involvement may be a rare manifestation of hereditary hemorrhagic telangiectasia but can be revealed by imaging modalities.
American Psychological Association (APA)
Takamatsu, Susumu& Sato, Kota& Kato, Shunsuke& Nagano, Hiroto& Ohtsukasa, Shunro& Kawachi, Yasuyuki. 2016. Splenic Involvement in Hereditary Hemorrhagic Telangiectasia. Case Reports in Medicine،Vol. 2016, no. 2016, pp.1-4.
https://search.emarefa.net/detail/BIM-1101085
Modern Language Association (MLA)
Takamatsu, Susumu…[et al.]. Splenic Involvement in Hereditary Hemorrhagic Telangiectasia. Case Reports in Medicine No. 2016 (2016), pp.1-4.
https://search.emarefa.net/detail/BIM-1101085
American Medical Association (AMA)
Takamatsu, Susumu& Sato, Kota& Kato, Shunsuke& Nagano, Hiroto& Ohtsukasa, Shunro& Kawachi, Yasuyuki. Splenic Involvement in Hereditary Hemorrhagic Telangiectasia. Case Reports in Medicine. 2016. Vol. 2016, no. 2016, pp.1-4.
https://search.emarefa.net/detail/BIM-1101085
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-1101085