Sacroiliitis and Polyarteritis Nodosa in a Patient with Familial Mediterranean Fever
Joint Authors
Ugan, Yunus
Doğru, Atalay
Şencan, Hüseyin
Şahin, Mehmet
Ercan Tunç, Şevket
Source
Issue
Vol. 2016, Issue 2016 (31 Dec. 2016), pp.1-3, 3 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2016-04-07
Country of Publication
Egypt
No. of Pages
3
Main Subjects
Abstract EN
Familial Mediterranean fever (FMF) is an autoinflammatory disorder with autosomal recessive inheritance, characterized by recurrent fever and episodes of serositis.
The condition is known to be caused by mutations in the MEFV (Mediterranean FeVer) gene, located in the short arm of chromosome 16.
While more than 310 sequence variants in the MEFV gene have been described to date, the diagnosis is still established clinically.
FMF may be accompanied by sacroiliitis and various forms of vasculitis.
The most common forms of associated vasculitis are Henoch-Schonlein purpura and polyarteritis nodosa (PAN).
We have presented here a fairly rare case of FMF, accompanied by both sacroiliitis and PAN.
American Psychological Association (APA)
Ugan, Yunus& Doğru, Atalay& Şencan, Hüseyin& Şahin, Mehmet& Ercan Tunç, Şevket. 2016. Sacroiliitis and Polyarteritis Nodosa in a Patient with Familial Mediterranean Fever. Case Reports in Medicine،Vol. 2016, no. 2016, pp.1-3.
https://search.emarefa.net/detail/BIM-1101120
Modern Language Association (MLA)
Ugan, Yunus…[et al.]. Sacroiliitis and Polyarteritis Nodosa in a Patient with Familial Mediterranean Fever. Case Reports in Medicine No. 2016 (2016), pp.1-3.
https://search.emarefa.net/detail/BIM-1101120
American Medical Association (AMA)
Ugan, Yunus& Doğru, Atalay& Şencan, Hüseyin& Şahin, Mehmet& Ercan Tunç, Şevket. Sacroiliitis and Polyarteritis Nodosa in a Patient with Familial Mediterranean Fever. Case Reports in Medicine. 2016. Vol. 2016, no. 2016, pp.1-3.
https://search.emarefa.net/detail/BIM-1101120
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-1101120