Isolated Intracranial Rosai-Dorfman Disease
Joint Authors
Taufiq, Md.
Khair, Abul
Begum, Ferdousy
Akhter, Shabnam
Shamim Farooq, Md.
Kamal, Mohammed
Source
Case Reports in Neurological Medicine
Issue
Vol. 2016, Issue 2016 (31 Dec. 2016), pp.1-4, 4 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2016-02-02
Country of Publication
Egypt
No. of Pages
4
Main Subjects
Abstract EN
Background.
Rosai-Dorfman disease (RDD) is a benign histiocytic proliferative disorder of unknown etiology.
This rare condition commonly causes massive cervical lymphadenopathy.
Intracranial RDD without any nodal involvement is extremely rare.
Case Report.
A young Bangladeshi male complained of bilateral complete blindness with left sided deafness for about three years.
There was no lymphadenopathy.
MRI and CT scan of brain suggested an inflammatory/neoplastic (?meningioma) lesion located at left parasellar region which extended frontally to encircle both optic nerves and also to left prepontine area.
Histopathologically the lesion was diagnosed as RDD.
The patient was treated with steroid and significant clinical improvement observed.
Conclusion.
The prognosis of intracranial RDD is not poor.
It can be treated with surgery with or without corticosteroids, chemotherapy, and so forth.
But as the condition is extremely rare and often misdiagnosed, the clinician, radiologist, and histopathologist should have a suspicion in their mind about the possibility of RDD.
American Psychological Association (APA)
Taufiq, Md.& Khair, Abul& Begum, Ferdousy& Akhter, Shabnam& Shamim Farooq, Md.& Kamal, Mohammed. 2016. Isolated Intracranial Rosai-Dorfman Disease. Case Reports in Neurological Medicine،Vol. 2016, no. 2016, pp.1-4.
https://search.emarefa.net/detail/BIM-1101245
Modern Language Association (MLA)
Taufiq, Md.…[et al.]. Isolated Intracranial Rosai-Dorfman Disease. Case Reports in Neurological Medicine No. 2016 (2016), pp.1-4.
https://search.emarefa.net/detail/BIM-1101245
American Medical Association (AMA)
Taufiq, Md.& Khair, Abul& Begum, Ferdousy& Akhter, Shabnam& Shamim Farooq, Md.& Kamal, Mohammed. Isolated Intracranial Rosai-Dorfman Disease. Case Reports in Neurological Medicine. 2016. Vol. 2016, no. 2016, pp.1-4.
https://search.emarefa.net/detail/BIM-1101245
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-1101245