![](/images/graphics-bg.png)
Pauci-Immune Crescentic Glomerulonephritis in Connective Tissue Disease
Joint Authors
Rosenthal, Ann
Yeturi, Supraja
Cronin, Mary
Robin, Adam
Lorna, Campbell
Source
Issue
Vol. 2016, Issue 2016 (31 Dec. 2016), pp.1-6, 6 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2016-07-18
Country of Publication
Egypt
No. of Pages
6
Main Subjects
Abstract EN
Pauci-immune crescentic glomerulonephritis is commonly seen in ANCA-associated vasculitis but it is rarely seen during the course of other connective tissue diseases like lupus or Sjogren’s syndrome or MCTD.
We report 3 cases of pauci-immune crescentic glomerulonephritis in patients with connective tissue disease other than vasculitis.
We reviewed literature and made summary of previously reported cases of this rare entity.
Clinical and laboratory features of these patients varied widely, but most of patients have met criteria for lupus.
In this small population of patients there is no correlation with ANCAs.
Most of the patients were treated with aggressive immunosuppression and did well if they were treated early in the course of their disease.
One of our patients required renal transplant, but she presented late in the course of her disease, as evidenced by chronicity on her renal biopsy.
Whether these patients are overlap of vasculitis and other connective tissue diseases or to be considered as a separate entity is yet to be described.
Clinicians must be aware of these presentations because initial presentation can be severe.
American Psychological Association (APA)
Yeturi, Supraja& Cronin, Mary& Robin, Adam& Lorna, Campbell& Rosenthal, Ann. 2016. Pauci-Immune Crescentic Glomerulonephritis in Connective Tissue Disease. Case Reports in Rheumatology،Vol. 2016, no. 2016, pp.1-6.
https://search.emarefa.net/detail/BIM-1102684
Modern Language Association (MLA)
Yeturi, Supraja…[et al.]. Pauci-Immune Crescentic Glomerulonephritis in Connective Tissue Disease. Case Reports in Rheumatology No. 2016 (2016), pp.1-6.
https://search.emarefa.net/detail/BIM-1102684
American Medical Association (AMA)
Yeturi, Supraja& Cronin, Mary& Robin, Adam& Lorna, Campbell& Rosenthal, Ann. Pauci-Immune Crescentic Glomerulonephritis in Connective Tissue Disease. Case Reports in Rheumatology. 2016. Vol. 2016, no. 2016, pp.1-6.
https://search.emarefa.net/detail/BIM-1102684
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-1102684