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Treatment and Patient Reported Outcome in Children with Hirschsprung Disease and Concomitant Congenital Heart Disease
Joint Authors
Stenström, Pernilla
Hagelsteen, Kristine
Hasserius, Johan
Hedbys, Josefine
Graneli, Christina
Source
Issue
Vol. 2017, Issue 2017 (31 Dec. 2017), pp.1-8, 8 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2017-03-08
Country of Publication
Egypt
No. of Pages
8
Main Subjects
Abstract EN
Purpose.
Congenital heart disease (CHD) is reported to be associated with Hirschsprung disease (HD).
The aim was to evaluate any differences between children with HD with and without CHD, respectively, with regard to patient characteristics, medical care, and patient reported bowel function.
Method.
This is a retrospective chart study and a cross-sectional long-term follow-up of patients older than 4 years old, including all children with HD operated on with transanal endorectal pull-through (TERPT) at a tertiary center of pediatric surgery.
Information about patient characteristics, diagnostics, surgery, and medical care was compiled.
At long-term follow-up, bowel function was assessed by Bowel Function Score.
Results.
Included were 53 HD-patients, 13 with CHD and 40 without CHD.
Children with CHD more commonly presented with failure to thrive; 4 (23%) compared to those without CHD (0%) (p<0.01).
In the long-term follow-up, including 32 patients (6 with CHD), constipation was more commonly reported by children with CHD 5 (83%) than by children without CHD 4 (27%) (p=0.01).
No differences were shown in the other parameters such as fecal control and incontinence.
Conclusion.
HD-patients with CHD more commonly presented with failure to thrive and more frequently reported constipation than HD-patients without CHD.
The findings indicate that HD-patients with CHD might need special consideration in their initial care and long-term follow-up.
American Psychological Association (APA)
Hasserius, Johan& Hedbys, Josefine& Graneli, Christina& Hagelsteen, Kristine& Stenström, Pernilla. 2017. Treatment and Patient Reported Outcome in Children with Hirschsprung Disease and Concomitant Congenital Heart Disease. BioMed Research International،Vol. 2017, no. 2017, pp.1-8.
https://search.emarefa.net/detail/BIM-1134125
Modern Language Association (MLA)
Hasserius, Johan…[et al.]. Treatment and Patient Reported Outcome in Children with Hirschsprung Disease and Concomitant Congenital Heart Disease. BioMed Research International No. 2017 (2017), pp.1-8.
https://search.emarefa.net/detail/BIM-1134125
American Medical Association (AMA)
Hasserius, Johan& Hedbys, Josefine& Graneli, Christina& Hagelsteen, Kristine& Stenström, Pernilla. Treatment and Patient Reported Outcome in Children with Hirschsprung Disease and Concomitant Congenital Heart Disease. BioMed Research International. 2017. Vol. 2017, no. 2017, pp.1-8.
https://search.emarefa.net/detail/BIM-1134125
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-1134125