Evaluation and Management of Unexpected Functional Rudimentary Uteri in Mayer–Rokitansky–Küster–Hauser Syndrome of Chinese Women
Joint Authors
Zhu, Lan
Deng, Shan
Tian, Qinjie
Source
Issue
Vol. 2020, Issue 2020 (31 Dec. 2020), pp.1-7, 7 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2020-11-24
Country of Publication
Egypt
No. of Pages
7
Main Subjects
Abstract EN
Objective.
To elucidate the characteristics of symptomatic attack of rudimentary uteri in MRKH syndrome and highlight the rare and unexpected possibilities.
Methods.
A cohort of 202 Chinese MRKH syndrome patients admitted to the Peking Union Medical College Hospital from Jan 2009 to Dec 2016 was analyzed retrospectively.
Based on the symptoms of abdominal pain before vaginoplasty, the patients were categorized into the asymptomatic and symptomatic groups.
Results.
Totally, 21 patients had their uteri removed due to obstructive bleeding, 19 of them had symptoms of abdominal pain before vaginoplasty, the mean duration of abdominal pain before artificial vaginoplasty was 5.0 years (range, 0.5–10 years), and the mean age at first onset of recurrent abdominal pain was 14.3 years old (range 11–18).
Two special cases showed unusual long incubation periods up to 23 years.
Ultrasound detected endometrioid echo in four asymptomatic patients.
Among the symptomatic group, 7 patients had no imaging evidence for endometrial cavities despite clinical pain.
Two of them developed severe symptoms over the next two or four years and eventually had their uteri removed.
Two patients reported persistent abdominal pain with a visual analog scale (VAS) score of 4–5, still under observation.
Three patients were lost to follow-up.
Conclusion.
More than 10% of the patients with MRKH syndrome had surgical indication to remove the rudimentary uteri.
The discrepancy between clinical symptoms and imaging calls for the vigilance for prophylactic surgery or prolonged follow-up.
American Psychological Association (APA)
Deng, Shan& Zhu, Lan& Tian, Qinjie. 2020. Evaluation and Management of Unexpected Functional Rudimentary Uteri in Mayer–Rokitansky–Küster–Hauser Syndrome of Chinese Women. BioMed Research International،Vol. 2020, no. 2020, pp.1-7.
https://search.emarefa.net/detail/BIM-1136219
Modern Language Association (MLA)
Deng, Shan…[et al.]. Evaluation and Management of Unexpected Functional Rudimentary Uteri in Mayer–Rokitansky–Küster–Hauser Syndrome of Chinese Women. BioMed Research International No. 2020 (2020), pp.1-7.
https://search.emarefa.net/detail/BIM-1136219
American Medical Association (AMA)
Deng, Shan& Zhu, Lan& Tian, Qinjie. Evaluation and Management of Unexpected Functional Rudimentary Uteri in Mayer–Rokitansky–Küster–Hauser Syndrome of Chinese Women. BioMed Research International. 2020. Vol. 2020, no. 2020, pp.1-7.
https://search.emarefa.net/detail/BIM-1136219
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-1136219