Melanotic Schwannoma of the Vagina: A Report of a Very Rare Tumor and Review of the Literature

Abstract EN

Melanotic schwannoma (MS) is a rare nerve sheath tumor with fewer than 200 cases reported.

MS has uncertain malignant potential and comprises 1% of all nerve sheath tumors with a predilection for the spinal nerve roots.

An even rarer location for this tumor is the vagina.

Up to 55% of MSs that contain psammoma bodies are associated with the Carney complex, an autosomal dominant syndrome.

Criteria for malignancy in MS are still not well established and long term follow-up of patients is recommended.

A 26-year-old woman presented with a bleeding vaginal tumor which was diagnosed as MS following excision.

The clinical, histopathological, and immunohistochemical features of this tumor are discussed.