Mixed Acinar-Endocrine Carcinoma (MAEC)‎ Arising in Duodenal Pancreatic Heterotopia

Abstract EN

Mixed acinar-endocrine carcinoma (MAEC) of the pancreas is a rare neoplasm, consisting of at least 25%–30% of acinar and neuroendocrine populations.

Patients are often middle-aged and present with nonspecific symptoms.

Imaging typically reveals a solid lesion in the pancreatic head.

Management involves surgical resection and the overall prognosis is variable.

Here, we present a case of a 48-year-old male who presented with a MAEC arising from duodenal pancreatic heterotopia.

This is the one of the first cases, with histologic evidence, of MAEC arising from pancreatic heterotopia.