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Euglycemic Ketoacidosis in Spinal Muscular Atrophy
Joint Authors
Papaioannou, Nikos
Theofanidou, Sofia
Iasonidou, Christina
Kapravelos, Nikolaos
Petridis, Nikolaos
Spyridonidou, Christina
Stoimenis, Dimitrios
Source
Issue
Vol. 2019, Issue 2019 (31 Dec. 2019), pp.1-3, 3 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2019-01-27
Country of Publication
Egypt
No. of Pages
3
Main Subjects
Abstract EN
Euglycemic ketoacidosis is defined by the triad of high anion gap acidosis, increased plasma ketones, and the absence of hyperglycemia.
Apart from diabetes mellitus, the disorder may occur in prolonged fasting, excessive alcohol consumption, pregnancy, and inborn errors of metabolism.
Here, we highlight the diagnosis of euglycemic ketoacidosis in a pediatric nondiabetic patient with spinal muscular atrophy (SMA) type 1 (Werdnig–Hoffmann disease), who, subsequently to her postoperative admission to the intensive care unit following a spinal surgery, developed high anion gap metabolic acidosis.
We discuss the pathophysiology of acid-base disorders in SMA, along with the glucose and fatty acids metabolism, the necessary knowledge for medical practitioners.
American Psychological Association (APA)
Stoimenis, Dimitrios& Spyridonidou, Christina& Theofanidou, Sofia& Petridis, Nikolaos& Papaioannou, Nikos& Iasonidou, Christina…[et al.]. 2019. Euglycemic Ketoacidosis in Spinal Muscular Atrophy. Case Reports in Pediatrics،Vol. 2019, no. 2019, pp.1-3.
https://search.emarefa.net/detail/BIM-1143663
Modern Language Association (MLA)
Stoimenis, Dimitrios…[et al.]. Euglycemic Ketoacidosis in Spinal Muscular Atrophy. Case Reports in Pediatrics No. 2019 (2019), pp.1-3.
https://search.emarefa.net/detail/BIM-1143663
American Medical Association (AMA)
Stoimenis, Dimitrios& Spyridonidou, Christina& Theofanidou, Sofia& Petridis, Nikolaos& Papaioannou, Nikos& Iasonidou, Christina…[et al.]. Euglycemic Ketoacidosis in Spinal Muscular Atrophy. Case Reports in Pediatrics. 2019. Vol. 2019, no. 2019, pp.1-3.
https://search.emarefa.net/detail/BIM-1143663
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-1143663