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Refractory Hepatic Hydrothorax: A Rare Complication of Systemic Sclerosis and Presinusoidal Portal Hypertension
Joint Authors
Horton, Samuel R. W.
Abrams, Gary A.
Chapman, Robert
Source
Issue
Vol. 2018, Issue 2018 (31 Dec. 2018), pp.1-4, 4 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2018-04-30
Country of Publication
Egypt
No. of Pages
4
Main Subjects
Abstract EN
We report on a rare case of refractory hepatic hydrothorax in an individual with Scleroderma/CREST syndrome and noncirrhotic portal hypertension.
Portal pressure measurements revealed a normal transjugular hepatic venous portal pressure gradient, mild pulmonary hypertension, and an unremarkable liver biopsy except for mild sinusoidal dilation.
Pulmonary hypertension, cardiac diastolic dysfunction, and chronic kidney disease were determined to be the causes of his refractory pleural effusions and ascites.
Over the year, he underwent 50 thoracenteses and 20 paracenteses averaging 10–12 liters/week.
Repeat pulmonary evaluation determined his pulmonary pressures to be normal and a secondary review of the “unremarkable” liver biopsy noted mild venous outflow obstruction and possibly Nodular Regenerative Hyperplasia (NRH).
Repeat portal pressures indirectly and directly confirmed the existence of presinusoidal portal hypertension that has been associated with NRH.
A transjugular intrahepatic portal systemic shunt (TIPS) was placed and he has not required thoracentesis or paracentesis over the past 18 months.
American Psychological Association (APA)
Abrams, Gary A.& Chapman, Robert& Horton, Samuel R. W.. 2018. Refractory Hepatic Hydrothorax: A Rare Complication of Systemic Sclerosis and Presinusoidal Portal Hypertension. Case Reports in Hepatology،Vol. 2018, no. 2018, pp.1-4.
https://search.emarefa.net/detail/BIM-1144196
Modern Language Association (MLA)
Abrams, Gary A.…[et al.]. Refractory Hepatic Hydrothorax: A Rare Complication of Systemic Sclerosis and Presinusoidal Portal Hypertension. Case Reports in Hepatology No. 2018 (2018), pp.1-4.
https://search.emarefa.net/detail/BIM-1144196
American Medical Association (AMA)
Abrams, Gary A.& Chapman, Robert& Horton, Samuel R. W.. Refractory Hepatic Hydrothorax: A Rare Complication of Systemic Sclerosis and Presinusoidal Portal Hypertension. Case Reports in Hepatology. 2018. Vol. 2018, no. 2018, pp.1-4.
https://search.emarefa.net/detail/BIM-1144196
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-1144196