Pleomorphic Pulmonary Manifestations of IgG4-Related Disease

Abstract EN

Immunoglobulin G4-related disease (IgG4-RD) is a fibroinflammatory disorder which has been first reported in 2001 by Hamano and colleagues in a patient with autoimmune sclerosing pancreatitis.

Almost every organ in the human body can be affected by IgG4-RD from infiltration with IgG4-positive plasma cells.

Involvement of lungs with IgG4 is reported previously, but still, there is no clear picture of the pathophysiology behind lung involvement.

Here, we are presenting a patient who has IgG4-RD presenting as pseudotumor of the lungs.