Giant Gastroschisis with Complete Liver Herniation: A Case Report of Two Patients
Joint Authors
Svetanoff, Wendy Jo
Zendejas, Benjamin
Demehri, Farokh R.
Cuenca, Alex
Nath, Bharath
Smithers, C. Jason
Source
Issue
Vol. 2019, Issue 2019 (31 Dec. 2019), pp.1-8, 8 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2019-01-15
Country of Publication
Egypt
No. of Pages
8
Main Subjects
Abstract EN
Introduction.
There are no reported survivors of gastroschisis with complete liver herniation.
We describe a case report of two patients, one of whom survived.
Case #1.
The patient was born with gastroschisis and herniation of the entire liver.
Along with silo placement, the abdominal fascia was attached to an external traction system for growth.
Complete closure was achieved at 5 months.
Due to pulmonary hypoplasia, high-frequency ventilation was required.
The patient is doing well, on a home ventilator wean, at 20 months.
Case #2.
The patient was born prematurely with gastroschisis, total liver herniation, and a defect extending to the pericardium.
A silo was attached to the fascia to provide growth of the abdominal cavity.
The patient developed respiratory failure, diffuse anasarca, and renal failure.
She died at 38 days of life.
Discussion.
We report the first survivor of gastroschisis with complete liver herniation, contrasting it with a death of a similar case.
The associated pulmonary hypoplasia may require long-term ventilation, the inflammatory response can lead to anasarca, and renal injury can occur from acute-on-chronic compartment syndrome.
Conclusion.
External fascial traction systems can help induce growth of the abdominal wall, allowing closure of the challenging abdomen.
While critical care management is complex, survival is possible.
American Psychological Association (APA)
Svetanoff, Wendy Jo& Zendejas, Benjamin& Demehri, Farokh R.& Cuenca, Alex& Nath, Bharath& Smithers, C. Jason. 2019. Giant Gastroschisis with Complete Liver Herniation: A Case Report of Two Patients. Case Reports in Surgery،Vol. 2019, no. 2019, pp.1-8.
https://search.emarefa.net/detail/BIM-1144762
Modern Language Association (MLA)
Svetanoff, Wendy Jo…[et al.]. Giant Gastroschisis with Complete Liver Herniation: A Case Report of Two Patients. Case Reports in Surgery No. 2019 (2019), pp.1-8.
https://search.emarefa.net/detail/BIM-1144762
American Medical Association (AMA)
Svetanoff, Wendy Jo& Zendejas, Benjamin& Demehri, Farokh R.& Cuenca, Alex& Nath, Bharath& Smithers, C. Jason. Giant Gastroschisis with Complete Liver Herniation: A Case Report of Two Patients. Case Reports in Surgery. 2019. Vol. 2019, no. 2019, pp.1-8.
https://search.emarefa.net/detail/BIM-1144762
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-1144762