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Macrophage Activation Syndrome, Glomerulonephritis, Pericarditis, and Retinal Vasculitis as Initial Presentation of Systemic Lupus Erythematosus
Joint Authors
Arevalo, Ana B.
Luo, Yiming
Wen, Yumeng
Dahal, Punya
Leuprecht, Lorenz
Bsrat, Makda
Source
Issue
Vol. 2018, Issue 2018 (31 Dec. 2018), pp.1-5, 5 p.
Publisher
Hindawi Publishing Corporation
Publication Date
2018-09-26
Country of Publication
Egypt
No. of Pages
5
Main Subjects
Abstract EN
Macrophage activation syndrome (MAS) is a rare manifestation of systemic lupus erythematosus (SLE) with potentially life-threatening consequences.
To the best of our knowledge, this is the first case reported in literature for a constellation of MAS, glomerulonephritis, pericarditis, and retinal vasculitis as initial presentation of SLE.
Despite extensive multisystem involvement of his disease, the patient responded well to initial steroid treatment, with mycophenolate mofetil successfully added as a steroid-sparing agent.
Our case highlights the importance of multispecialty collaboration in the diagnosis and management of SLE with multisystem involvement.
American Psychological Association (APA)
Luo, Yiming& Wen, Yumeng& Arevalo, Ana B.& Dahal, Punya& Leuprecht, Lorenz& Bsrat, Makda. 2018. Macrophage Activation Syndrome, Glomerulonephritis, Pericarditis, and Retinal Vasculitis as Initial Presentation of Systemic Lupus Erythematosus. Case Reports in Medicine،Vol. 2018, no. 2018, pp.1-5.
https://search.emarefa.net/detail/BIM-1144991
Modern Language Association (MLA)
Luo, Yiming…[et al.]. Macrophage Activation Syndrome, Glomerulonephritis, Pericarditis, and Retinal Vasculitis as Initial Presentation of Systemic Lupus Erythematosus. Case Reports in Medicine No. 2018 (2018), pp.1-5.
https://search.emarefa.net/detail/BIM-1144991
American Medical Association (AMA)
Luo, Yiming& Wen, Yumeng& Arevalo, Ana B.& Dahal, Punya& Leuprecht, Lorenz& Bsrat, Makda. Macrophage Activation Syndrome, Glomerulonephritis, Pericarditis, and Retinal Vasculitis as Initial Presentation of Systemic Lupus Erythematosus. Case Reports in Medicine. 2018. Vol. 2018, no. 2018, pp.1-5.
https://search.emarefa.net/detail/BIM-1144991
Data Type
Journal Articles
Language
English
Notes
Includes bibliographical references
Record ID
BIM-1144991